Zempilo, Diseases and nemibandela
Hypertelorism - yintoni na le nto? Oonobangela kunye neempawu
Hypertelorism - igama, ngawo ukuthini a ngezifo esibonakala ukwanda kakhulu kwi kumgama phakathi kwamalungu amabini nesithandwa sakhe. Kwiimeko ezininzi kwafunyaniswa hypertelorism ocular, kodwa ezinye utshintsho zophendlo lwezifo kwi yezonyango yangoku. Oku koko ukuchaza kamva kweli nqaku.
Hypertelorism - yintoni na le nto?
Eli binzana eqhelekileyo iingxelo zonyango. Hypertelorism - kukuthi, njengokuba sele kukhankanyiwe, a ngezifo leyo ukhatshwa kukwanda kumgama phakathi kwamalungu amabini nesithandwa sakhe. Kufuneka kuqatshelwe ukuba inkcazelo waqalisa kusetyenziselwa kwakude kudala -, kwabonakala okokuqala kwiimpapasho lwaseburhulumenteni 1924.
Ngokomzekelo, xa amayeza eyaziwa njenge ngezifo ezifana ingono hypertelorism. Kulo mzekelo, yaphula ekuthiwa umbele Index - isalathiso, nto leyo umiselwa umlinganiselo phakathi manani achazwe apha esifubeni kwinqanaba le ingono kunye umgama phakathi kwabo. Pathology ayikho ezimele rhoqo ukuvela imvelaphi malformations iziphene, ezifana Apert syndrome, isifo Edwards '.
Kodwa zixhaphakileyo Orbital hypertelorism - isifo apho kukho ukwanda ezingaqhelekanga umgama phakathi neziseko iliso. Loo state isegazini - oko banesifo ngemihla kwangoko emva kokuzalwa.
Zintoni izinto ezibangela izifo
Hypertelorism eye - iziphene disorder, nto leyo idla ezinxulumene ezahlukeneyo izifo yemfuza. Umzekelo, neziseko eye ngokubanzi kakhulu bebekwe kuvandlakanywa abantwana nefrofibromatozom, Apert syndrome, Down syndrome, Thowusti, Edwards kunye nezinye izifo ezininzi zihamba malformations emininzi olungekazalwa. Ngenxa yezizathu efanayo ngqo ziquka ukungaqheleki ezahlukeneyo kubume ubuchopho okanye ukhakhayi - kuba phambi yamathumba, ukuphiliswa ngokukhawuleza kakhulu iinxalenye yokakayi, herniation ingqondo zonxinzelelo nemingxuma.
Kakade ke, kusenokwenzeka ukuba abanye ubungozi ukuba uphazamise eqhelekileyo uphuhliso siswini , okanye kubangele ziyafumaneka ukungaqheleki genetic Palsy. Ngoko ke, lo nefuthe elibi kwi imeko yomntwana yachatshazelwa usulelo kukhutshelwa yi unina ngexesha lokukhulelwa, kwakunye ukungena umzimba ityhefu, kubandakanywa amachiza enzima, ngeedosi eziphezulu utywala, iziyobisi njalo njalo. D.
Hypertelorism: photo nezinxulumene iimpawu
Kuthiwa hypertelorism na iqondo ezahlukeneyo - ezinye izigulane iliso asuswa kancinci kuphela, ngoxa kwezinye avulekela ngaphandle kunye nogqirha wakho siqaphela isiphako emva look lokuqala usana olo. Ezi abantwana iimpawu uphawu kakhulu zobuso lobume:
- umgama Pathologically omkhulu phakathi ubuso obusezintongeni ezo iziseko.
- Amaxesha amaninzi deformation palpebral ehlola wayibona - kungenzeka ube imilo mgaqweni, okanye azilingani iingqameko kakhulu.
- Kukho kwakhona isakhiwo uphawu empumlo - umva yakhe tyaba yaye ububanzi impumlo kwebhulorho.
- Amaninzi kunye hypertelorism ebantwaneni kwafunyaniswa strabismus, iintlobo of ongaboniyo, lo deformation le luvo optic, le ngxaki ivumba.
Ngelishwa, ezi mpawu zingentla yemfuza iimpawu kuphela ukugxojwa isakhiwo ngaphambili yokakayi. Amaxesha amaninzi, abantwana babe sengozini ngeenyawo, uphuhliso okungaqhelekanga le imihlathi, uphuhliso kakuhle ngokwasengqondweni.
iindlela zokuxilonga
Kakade ke, kulo mzekelo, kubaluleke kakhulu ukuba ukuxilonga ngokuchanekileyo, kuba ufuna ukufumanisa ubukho sisifo ethile yemfuza. Doctor ubala le interorbit okruzhnostnoy-indeksi, nto leyo umiselwa ngokwahlula intloko achazwe apha esilinganiselweyo kumgama phakathi iikona yangaphakathi ngamehlo slits, kwaye inani engumphumela liphindaphindwe 100 leengxaki ngokubanzi wathi kwimeko apho index lidlula 6.8 .
Ngaphezu koko kwenziwa abazali anamnesis uphando lwemfuzo. Kwakhona, qiniseka umntwana wakho emiselweyo livakale Imagnethi okanye Itomography ayifum yentloko - le nkqubo ukungaphili ithambo kunye ubukho yamathumba engqondweni.
unyango lwezifo
Ukuba sithethe hypertelorism, ngoko unyango oluthile iyafuneka kuphela apho kukho ingxaki enkulu amaziko umbono-luvo neziphelo. Kule meko kucetyiswa uqhaqho. Ngexesha inkqubo, ugqirha owenza skull zeplastiki. Kodwa ke, isigqibo sokubamba msebenzi kuthatha specialist, ukunikela ingqalelo kwizinto ezininzi, kuquka imeko kunye nobukho comorbidities zomntwana. Surgery yenziwa phambi kokuba isigulane kwiminyaka emibini ubudala - eli lixesha lo msebenzi unika iziphumo kakhulu kangangoko.
Ke ukuba unyango systemic, oko sibhekiswe ulungiso sifo zaseprayimari. Ukususela kule kwaye ixhomekeke unyango zonyango.
Uthintelo izifo kunye abane kwizigulane
Hypertelorism - kunoko, yinto siphene kubuhle. Iingozi ziquka syndromes kunye nezifo ezo zihamba sigulo. Ngoko ke, isiphako ngokwayo akukho kusisisongelo kubomi bomntwana. Ezi nketho kuphela ngabo iimeko apho iziseko iliso ukonakala kuchaphazela umbono yesigulane.
Ngokuphathelele kuthintelo, indlela ngelishwa ezithile zokuthintela ptologii ezichazwe ayisekho. Ukucutha umngcipheko zizifo intrauterine, ngexesha lokukhulelwa kufuneka esweni ngenyameko impilo, nidle okulungileyo, ukuyeka ukutshaya, utywala, iziyobisi kunye neziyobisi ezinokuba yingozi.
Ukucwangcisela ukukhulelwa kwaye kufuneka siphathwe ngenkathalo ukuba angandishiyi ezingxoxo ecwangcisiweyo nge zofuzo u. Ezinye izifo zofuzo ukuba yintoni na unobangela nkqu Esibelekweni. Uphando yemfuza ngexesha ucwangciso lokukhulelwa kunceda ubone amathuba okuba umntwana unxaxho.
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