ZempiloDiseases and nemibandela

Klein syndrome - Levin: Oonobangela, Iimpawu and Treatment

Klein syndrome - Levin - yinto kuphazamiseka nezolo luphawulwa kumaxa zokulala kunye uphaphama. ubude bayo ziyahluka ukusuka imini enye ukuya kwiiveki 2-3. Isigulane uyavuka iiyure ezimbalwa, ngaxeshanye uziphethe kakuhle yaye uva ezikwenza ukudla. Esi ngezifo inqabile, kodwa iimpawu zayo engaqhelekanga, yena ezitsala ingqalelo izazinzulu ezininzi.

ulwazi jikelele

Sisihlandlo sokuqala ongaqhelekanga syndrome yomhla we-1925. A wezifo zengqondo saseJamani Villi Kleyn ichazwe ngokweenkcukacha kwiimeko eziliqela "isiCoci-" phakathi izigulane zabo. Kamva, ngowe-1936, i-umphandi American Max Levin wongezelela ingqalelo oogxa bakhe Imigqaliselo ezintsha ezintlanu Ukuphazamiseka uphaphama kunye ukungaqheleki zesondlo. Kungekudala ngezifo ifumana igama lawo amagama oosonzululwazi ezimbini.

Klein syndrome - Levin, nangona nokunqaba wayo, buchazwe njengokuba sisifo esahlukileyo kwezinye zokulala. Okukhona Ukubhenca amadoda iminyaka 15-25 ubudala. Kuphela nje iimeko zonyango ezimbalwa echazwe amantombazana ezidalwa ubudala. Ngokutsho izazinzulu, bonke bephela zibangelwa ukuhla nokunyuka kwinqanaba dlala emzimbeni.

Izizathu

Njani na syndrome Kleine - Levin? Le umyalezo wahlala ayaziwa de kutshanje. Ngenxa kuphuhliso yenzululwazi, okanye mandithi yimbonakalo i ungcoliseko Itomography, ezinye izazinzulu nokucingela kubo kwaqinisekiswa.

Phakathi Iimbangi ezingundoqo iingcali sifo ukuchonga kwekhono ye ukuyilwa reticular yengqondo kunye ngxenye. Enye into edlalwe yi hormone litshintsha umzimba, nto ingqinwa efumanise wesifo phakathi abafikisayo amadoda namabhinqa. A indima edlalwe sisifo wentsholongwane egazini, ukwenzakala ebuchotsheni esibuhlungu, ukwanda nidloba xa lobushushu emzimbeni. izigulane ezininzi zaqala ikhonkco yemfuza. amalungu eentsapho uphethwe ekubonakalisweni njengesifo enqabileyo enjalo.

Akwenzeki ukuba yeyiphi kwezi zinto zidlala indima enkulu kuphuhliso isifo. izazinzulu ezininzi uyavuma ukuba le Pathogenesis esi sifo onesiphene yemfuza ekumiseleni umsebenzi hypothalamic, nto leyo isebenza phantsi kweempembelelo ukuphazamiseka kwamadlala kwi ukufikisa.

Umfanekiso clinical jikelele

Klein syndrome - Levine luphawulwa iziqephu ubuthongo elide (malunga 20 iiyure). Zazindiphazamisa kuphela ngokwanelisa iimfuno zendalo. Zivuse isigulana ngeli xesha akunakwenzeka. kuhlaselwa ingahlala ukusuka kwiintsuku ezimbalwa ukuya kwiiveki ezimbini. Uncwadi lonyango ichaza xa elona xesha lininzi "isiCoci-" yenzeka kwiintsuku 42.

ixesha ngasinye ukuthwala ubuthongo ayiphelelanga. Indoda leyo ayiyi kuphumla, futhi belele kwakhona emva Awakening ngamnye ngenxa yokungabikho bamandla uyawa. Xa episode iphela, isigulana uvakalelwa ingqiqo ngamandla ngenxa yendlala. Yena uqala ukudla yonke into eza indlela yakhe. Emva kokufezekisa bendlala isigulane uya kulala kwakhona.

Yintoni enye ine syndrome Klein - iimpawu Levin? okwexesha elifutshane uphaphama wambi ekhatshwa ndlongondlongo okugqithisileyo kwaye nochuku, nemibono. Xa ukuqhubela phambili iphela, isigulane ngcembe abuyele isantya eqhelekileyo yobomi. Unako akayikhumbuli kakhulu imihla yokugqibela ezimbalwa okanye iiveki, bekholelwa ukuba walala ubusuku enye kuphela. ukuhlasela Ngaphandle umntu ukhangela ziphilile. Noko ke, malunga nemvelaphi iphango eyenzeke ngayo ubunzima bomzimba kwandisa.

unyango

irejimeni Clear kule sifo ayikho ngenxa yezizathu ezibini. Okokuqala, ukuba ubulawe nto leyo kutyhilwa. Okwesibini, zokugula idla umva ngokuzenzekelayo. Ngoko ke, oogqirha abaninzi musa sibone imfuneko unyango ngamachiza.

"IsiCoci-" emva kweeveki ezimbalwa, nendlala okungalawulekilyo - ezi iimpawu ukuchaza ngqo syndrome Kleine - Levin. Unyango ibhalwa apho izifo ezinjalo ukuba izalamane ukungaphatheki isigulane. Ziziphi amayeza lalathelwe ukuba izigulane? Ngokuqhelekileyo, oko antipsychotics, okudambisa kunye nemithi yokunciphisa. Ezi mali zibizwa ngamnye ngokuphathelele uhlobo esi sifo. Imvukelo ukusebenzisa kwabo inceda ukwehlisa inani ukuhlaselwa, kunegalelo ukuze kuxolelwe ixesha elide. Iziyobisi kufuneka isetyenziswe kuphela nje unyango nomqondiso. Banceda nje kuphela isigulane, njengoko intsapho yakhe uphile ixesha buhlungu.

Outlook

Klein syndrome - Levin, ukubonakala ngesiquphe, ngokuthe ngcembe kunciphisa obubonakala. Kuthetha ntoni oku? Ekuhambeni kwexesha, ukuhlaselwa azikho nje ixesha elide, kwaye ekhefu phakathi kwabo ukwandisa. Ngenxa yoko, esi sifo ngokuzenzekelayo nya, kungasali iingxaki zempilo ebonakalayo.

Ngamafuphi

Ke kaloku, ukuba uyazi ukuba yintoni na syndrome Kleine - Levin iimpawu. Oonobangela yale sifo ayiqondwa ngokupheleleyo. zonyango echukumisayo ayilibaleki kuphuhliswa. Abaguli kwafuneka lijongane maxa bubuthongo elide kunye ukutya ngokugqithiseleyo, kufuneka unyamezele nje kubo. Pathology kuphetha alulame ngokupheleleyo. Okwangoku, oosonzululwazi isebenza ngomba yokudala unyango olumandla onaso.

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