Zempilo, Diseases and nemibandela
Wegener kaThixo granulomatosis - Oonobangela, iimpawu, unyango.
granulomatosis Wegener kaThixo - i sisifo samathambo luphawulwa ukudumba kwemithambo ezincinane ngemithambo. Kwiimeko ezininzi kwemithambo asha Ukubonelela igazi sinuses, wemiphunga kwizintso iithishu kodwa ke, ukongezelela, kukho iimilo buso kwimeko kuchaphazela kuphela enye yezi imimandla. Nge granulomatosis olubanzi phantse lonke nqa yi zombini imiphunga kunye nezintso zombini. Xa kunjalo, ukuba nale ukukhanya kuphela okanye kuphela nezintso, loo nto sisifo ekuthiwa granulomatosis Wegener kaThixo ayiphelelanga.
granulomatosis Wegener kaThixo ixhaphake kakhulu kubantu abatsha okanye eliqina, phantse ngaphandle ukuhlangabezana abantwana. Kodwa ke, nangona kunjalo, esi sifo uyakwazi kuchaphazela onke amaqela ubudala. manani Gender kuyilwa le sifo eyahlukileyo abalobi ezahlukeneyo.
Ezibangela isifo
Izinto ezibangela izifo ezifana, ezifana granulomatosis Wegener kaThixo, namhlanje akukaqondwa kakuhle. Iingcali ezininzi zikholelwa ukuba unobangela sifo inokuba arhente wentsholongwane egazini, ngokuba granulomatosis Wegener zidla kwenzeka emva kogonyo, SARS, unyango zintsholongwane okanye sesichengeni. Kodwa ke, ngelishwa, i-arhente ngeentsholongwane nangoku awabelwa, ngoko ke esi sifo njengento sokuhlasela.
Ezinye izigulane xanisa poradenitis kunye granulomatosis Wegener kaThixo. Kufuneka kuqondwe ukuba ukufana iimpawu izifo ezimbini ezahlukeneyo ngokupheleleyo kuba poradenitis kuvela ngenxa ngamagciwane bacteria (chlamydia), lo gama granulomatosis Wegener kaThixo sisifo samathambo.
Iimpawu kunye nefomu izifo
granulomatosis Wegener kunokuba kuqalisa ngesiquphe, kodwa kwaqala kancinci. Uphawu lokuqala zale sifo kuqwalaselwa lobushushu subfebrile, ngoko oko kunciphisa onombilini. Emva koko lobushushu eqalisa ukuphakama, yaye inkqubela isifo.
Iimpawu eziqhelekileyo kwesi sifo zibandakanya:
- komzimba;
- nokudinwa;
- ekunyuseleni ubushushu;
- iintlungu kwamalunga;
- intlungu komtshiso oko sinus.
Ukongeza, esi sifo kuchaphazela iinxalenye ezahlukeneyo omzimba, sinikela iimpawu eyahlukileyo ngokupheleleyo. Umzekelo, kunye ngokoyiswa zangaphandle impumlo yokuphefumla esihambisayo kunye ubovu iyantlukwano ezingemnandi liliphalaza igazi elimsulwa, isifo necrotic ngeempumlo, kwakunye inkalakahla ethambileyo kunye tonsils.
Ifom ngokubanzi isifo unika iinyanga ezimbalwa, kwingxaki kakhulu eluswini, ingakumbi, ukukhangeleka ukopha, nodular, izinto necrotic, kwaye kwezinye amaqela izigulane, kunye pericarditis, myocarditis okanye yomoya.
lokufunyaniswa kwesifo
Ngokuyintloko bethengisa izigulane granulomatosis Wegener kufuneka kudlule urinalysis ubukho protein negazi ezibomvu iiseli yokuchama. Further X-ray imifanekiso zenziwa sinuses nesifuba, ukubona utshintsho zophendlo lwezifo. Ngaphezu koko, uhlalutyo yegazi iyathathwa kwaye, ingakumbi, ujongwa ESR kunye neprothini C-izidubuli. Kukho kwakhona uhlalutyo kratya, kodwa kwakhona ngempumelelo ngakumbi ukuchonga izilwa antineyrofilnyh cytoplasmic.
unyango lwesifo
granulomatosis Wegener kaThixo, ngaphandle unyango olufanelekileyo isigulane kungakhokelela kakuhle ekufeni kwisithuba iinyanga ezimbini ukuya kwezintathu. Yonke unyango kakhulu ezijoliswe kwezithandani kwamajoni omzimba, kwakunye ngayo arhabaxa yasekuhlaleni. Amachiza ithandwayo corticosteroids kunye cyclophosphamide. La machiza kufuneka athathwe de kuxolelwe esi sifo, kwaye ke akukho wehluleka isifo Hodgkin kaThixo, kungongezwa kubo kodwa kunye methotrexate, nekufuneka athathe isibini iminyaka.
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