Zempilo, Diseases and nemibandela
Isifo Darier esithi: oonobangela, iimpawu, unyango
Inkoliso yabantu i ezifanayo ngqo abazali babo. Omnye ufumana amehlo aluhlaza upopu, omnye - iinwele unina chic ngayo. Kakade ke, maxa wambi vice versa. Noko ke, sonke sikhula iziphumo umdla zofuzo izalamane zethu close imicu. Amaxesha amaninzi, amehlo ezinkulu, iinwele olugobileyo kunye nemilenze emide, abazali banike abantwana babo iseti izifo ezahlukeneyo. Bakwenza oku kungekhona njongo, nokuba ngaphandle kwemvume yakho. Pathology ingabi ubomi, kodwa kaninzi imeko yahlukile. Umntu uba bathinjwa yezifo usapho kunye izifo. Enye yezi "izipho" izifo Darier. Yintoni na? Yintoni ebangela le zokugula?
ulwazi jikelele
Phantsi isifo Darier xa kubhekiswa dermatosis njengelifa walibonakalisa irhashalala ngohlobo maqhuqhuva ngebala okanye mdaka. Yokuba ikhowuni-zime kunye wayifulela soma zamafu. Maqhuqhuva eyendayo phezu Imihlubulo emzimbeni ndawonye kwaye ibe inxeba efumileyo. Kuxhomekeka kwindawo izilonda imbonakalo yazo, isifo Darier kaThixo yahlulwe iintlobo ezine:
- Eyendayo. Lubonakala ngokuba lilungiselelo linear lamaziko apho kuhlawula kuphela kwiindawo lungako umzimba.
- Classical. Irhashalala becala eyendayo kwi entlonzeni, esifubeni neendlebe.
- Qwaba. Kunye maqhuqhuva standard kuvela papules polyhedral ofana intsumpa. Ngokuqhelekileyo, ukuba emva ezandleni nasezinyaweni.
- Vesicular-bullous. Olu hlobo esi sifo kunqabile kakhulu. Lubonakala yi izilonda ezininzi imfihlo ngaphaya. Baya kuvela ecaleni entanyeni, kuloo ndawo Imihlubulo yesikhumba enkulu.
izilonda Primary papules abafunyenwe kwizigulane abaphakathi kweminyaka iminyaka esibhozo ukuya kwelishumi elinesihlanu. kusehla isifo abadala kunqabile.
Izinto ezibangela izifo
Esona sizathu sokuba esi sifo phambi sofuzo ezingaqhelekanga, kwaye zinegalelo elikhulu umngcipheko - sifuze ilifa. Ngenxa yoko, Vitamin A yi kwelifunekayo ngokupheleleyo emzimbeni, umsebenzi enqanda ezithile kunye nesiqulatho nezinki kwi sangaphandle lifinyele. Le ngenxa yezi nkqubo zophendlo lwezifo kukwaphula indlela yesikhumba keratinization.
Ukuba umama okanye utata ezi abathwali sofuzo ezingaqhelekanga-50% amatyala, kubonakala ukukhanya umntwana unesifo "isifo Darier kaThixo." Noko ke, ukuba abazali izigulane azalwe nomntwana ophile ngokupheleleyo, le ngezifo asizidini abantwana bakhe elizayo. Esi sifo ayihambi ngamathontsi emoyeni okanye ngokwesondo.
picture clinical
Inkqubo yezifo iqala imbonakalo maqhuqhuva tyaba follicular, ezo ngenye indlela eyaziwa ngokuba papules. isayizi yazo ingahluka-1 ukuya ku-3 mm. Papules legqunyiwe uqweqwe esiluqilima umbala omdaka. Phantsi kwalo kukho misinga xa elimile ifanele. Maqhuqhuva zisendaweni imilomo zoboya, nto leyo maxa wambi kukhokelela kuphuhliso kwenye izifo - folliculitis. Ngoko ke, ngaphambi kokuba uqale unyango kuyimfuneko ukuqhuba isifo umahluko.
zilungiselelwe iqhuma symmetrically ambambe kummandla subclavian kunye iindawo flexor namalungu. Kwi entlonzeni papule kusikhumbuza umonakalo amade enamaxolo kunye soma. Emva kokuba ukususwa kwawo kwiindawo kuvela izilonda nakujoliso olutsha of alopecia. Njengoko esi sifo kukho irhashalala ezintsha kunye lweposi endala zibe kwindawo ethile.
iimviwo Medical
Lokufunyaniswa kwesifo isekelwe umfanekiso lwezonyango kunye imbali yezonyango olupheleleyo isigulane. Ngethuba loviwo, ugqirha ihlola iimpawu zesifo, iimeko zangaphambili irhashalala phakathi nezizalwane. Ukuze uqinisekise esi sifo yabelwe uhlalutyo histological yesikhumba biopsy. Uxilongo umahluko lwenziwa pemphigus kwiintsapho, papillomatosis kunye dermatitis seborrheic.
imigaqo yonyango
Unyango nale sifo ngokuqhelekileyo lwenziwa rhoqo kwesibhedlele. Ngexesha exacerbation yenkqubo zophendlo lwezifo ubonakala okanye zinabile ukwenzakala isigulane kufuna esibhedlele esibhedlele dermatological.
Isigulana kwanonyango nomqondiso. Zonke izigulane kunye kungekho ngaphandle eyabelwe vitamin A ngokohlobo isitofu ngomlomo okanye intramuscular. Izikali ibalwa ngamnye, kuthathelwa ingqalelo ubudala yesigulane. Ikhosi ye unyango idla iinyanga ezi-3, ke ngoko lixhuzule i ikhefu uphinde unyango.
Isiphumo HIV kunye nesifo Darier ukunika iibhate zamazwi kunye izicelo ngamafutha keratolytic. Phambi izilonda ezinkulu, ungenelelo utyando okanye electrocoagulation. Xa isifo Darier bukaThixo sikhatshwa kongezwe igciwane, i-zintsholongwane emiselweyo.
Ipredikshini kunye nokuthintela
Esi sifo sisasazwa kuphela lilifa. Kungenxa yoko le nto nje iingcali ephambili kuthintelo bacebisa kokubonisana zofuzo ukuya abatshatileyo planning ngexesha kufutshane ekhulelwe umntwana. Oku kuyinyaniso ingakumbi abazali, ngubani na entsatsheni sele kufunyaniswe isifo Darier kaThixo.
Unyango ezichazwe ngasentla, ngokuqhelekileyo ibonisa iziphumo ezihle. izigulane ezininzi ukufikelela kuma uxolelo iminyaka embalwa. Noko ke, umntu kufuneka asinakulindela bachache ngokupheleleyo.
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