Budd-Chiari syndrome

Budd-Chiari syndrome kwenzeka ngenxa obliteration eqhubela phambili (wokuvala okanye exineneyo) le mithambo ye Kwangale ekufunxeni esibindini. Chiari wayekholelwa ukuba esona sizathu - kukukrala ephambili yegazi hepatic. Kodwa kamva yayichongwe kwezinye iimeko, ngelixa thrombosis le mithambo hepatic kunye ophantsi Vena cava.

Le ncwadi ichaza malunga 200 amatyala lokutshabalalisa endoflebita in hepatic emithanjeni (isifo , Budd-Chiari syndrome).

Ngophuhliso thrombophlebitis arantsieva duct, nto leyo yenza ngqo kwi Kwangale hepatic ekhohlo, umthambo yosana, yaye esi sifo ukuze kukhule yabantwana yasekuqaleni. Iqokobhe engaphakathi yegazi hepatic okanye Vena obuphantsi Vienna (kufutshane intlanganisela kwesibindi) olukhulayo, maxa wambi uncediswa egazi. Konke oku kubangela ukuba ukuvalwa okanye licuthe le mithambo ye Kwangale, nto leyo, ebangela uphuhliso ngxi kunye ucinezelo kweeseli zesibindi.

Budd-Chiari syndrome kwakhona kwezinye izinto ezimbi: neoplasms amabi, kwesibindi, injeke, zezintso, njl, izifo nemithambo ngokubanzi indalo. Ngokoma Kwakhona igalelo licuthe yegazi hepatic. Chiari syndrome kunokubangela kwindawo eyendawo ethile Gunma echinococcosis, actinomycosis, amathumba njalo njalo.

Ngokwezonyango, Budd-Chiari syndrome ubonisa iimpawu zesi sifo engundoqo, oko kwabangela ukuba umboniso phambili nazo zixhomekeke ngethuba occlusion le mithambo. Imela phandle esibukhali kwaye ukuvela chu onaso.

Acute hepatic vein occlusion ebangela inkangeleko ngesiquphe ukugabha, iintlungu ikota yesangqa ekunene eliphezulu okanye epigastrium ngenxa ukudumba kwesibindi, kwakunye hyperextension Glisson Isingxobo, iphuhlisa ascites, kukho yellowness encinane.

lwegazi Portal nesifo ngexesha elinye ngenxa yokwanda okukhawulezayo uxinzelelo kwi sinusoids hepatic ngemithambo.

Ascites nesi sifo ayikho esinokunyangwa womchamo, ulwelo luyakha ngokukhawuleza kwakhona kakhulu emva paracentesis, maxa wambi ibhiyozelwa ukuba ungene igazi lakhe, ukuze babe hydrothorax. Ukuba ejoyina thrombosis ukuvela kwi Vena cava kunguhata, ngoko ke ukudumba apho yesiqephu asezantsi, "Medusa intloko ', kunye xi ukukhanya lisetyenziswa kuyo, igazi liya phezulu.

Ngophuhliso iyonke vein occlusion hepatic ejoyina thrombosis mesenteric, kukho iintlungu kunye nesifo sorhudo, iingxaki luvo abonakale ngenxa iseli isibindi kukwenzakala ezikhokelela ekufeni kwiintsuku nje ezimbalwa.

Ngamanye amaxesha syndrome Budd - Chiari, kunye nokuvalwa kwenxenye le mithambo ye Kwangale zingenzeka njenge sisifo esingapheliyo ixesha elide. Nendalo loo ukuhamba kwexesha kwenzeka ejikeleza akananto: zithambe ikhe ulusu umthambo, lwegazi portal livela, uze emva koko ajoyine ngemithambo esophageal varicose.

Kuba uphethwe ubukho kubalulekile yokwehla xi ngemithambo occlusal isibindi kunye nokwanda ngaxeshanye yengcinezelo portal, nto leyo ibanjiwe ngokusebenzisa iindlela hepato- kunye splenomanometrii. Used rentgenogepatografiya retrograde apho agents umahluko ebiqaliswe kwi Kusenjalo hepatic. uxilongo ultrasound isekelwe imiqondiso ngqo - imifanekiso igazi ihlwili ngemithambo.

Ngaphandle umbala izifundo doplerrovskogo lubonisa Budd-Chiari syndrome ku:

• Ubukho lotshintsho kwentamo esibindini, uphawu kakhulu zesibindi okunamafutha okanye abanesigulo ye ijwabu kwesibindi,

• I-mfanekiso akukho mithambo hepatic, inginginya umzekelo, ngenxa yobukho kwi mithambo echo-HIV kwi sayo,

• a licuthe le Vena cava obuphantsi,

• iimpawu lwegazi portal, ukuba esi sifo kuyoluka.