Zempilo, Diseases and nemibandela
Isifo Kawasaki
Kawasaki sifo kakhulu ezinqabileyo, ingakumbi kwilizwe lethu. elinye igama layo - giant cell arteritis. Ityala lokuqala kuchazwa 1967 eJapan, apho kude kube ngoku sifo kakhulu kuxhaphake kakhulu kunokuba kwamanye amazwe.
umyalezo wayo akukabikho ukuqonda ngokupheleleyo, kodwa arhente uqikelelo olukhoyo a Igciwane ebangela ukudumba imithambo yegazi emzimbeni womntu. Okubangel 'umdla kukuba sisifo Kawasaki Ichaphazela ikakhulu abantwana abangaphantsi kweminyaka-4 ubudala, buthathaka inkqubo yomzimba yokuzikhusela, yaye ngokufuthi ngaphezu amakhwenkwe. Kwilizwe lethu lokufunyaniswa "isifo Kawasaki" owaliweyo kunqabile, malunga amatyala B10 ngonyaka ngamnye. Nangona kunjalo, inani yokwenene ibe ngaphezulu, kuba asinguye wonke ugqirha akaphumeleli ukuba azazi iimpawu ubeke uxilongo echanekileyo.
Nakuba iintlobo ngeentlobo iimpawu, ukuxilonga ezibalulekileyo izinto ezimbalwa iingongoma eziphambili. isifo Kawasaki uqala ngokwanda lobushushu, leyo kubanjwa ukususela 5-10 ukuya 15-20dney. Izigulane ukuphuhlisa conjunctivitis, nto leyo ichaphazela amehlo omabini. Emva kweeveki ezimbini abaqala ulusu ezintendeni kunye kweentende etywiniweyo, blushes aze aqalise uxobule. Kuyenzeka ukuba isifo Kawasaki sikhatshwa kwamaqhakuvana kumalungu ezahlukeneyo omzimba, enxibe umlinganiswa polymorphous. Emva kwexesha, oko kutyhobozela, ize ithi shwaka. Ukuba ukhangela emlonyeni umntwana egulayo, unako ukufumana ekuthiwa "istrawberry" ulwimi dumbe, obomvu eqaqambileyo ngebala kunye nobukho hemorrhages encinane iintsini, ngaphakathi nemihlathi. Imilebe kwakhona zidumbe umbilini. Liphuhlisa hyperemia umqala, ingxinano ngeempumlo kwenzeka. Amaxesha amaninzi ngesandla esinye kwiindawo entanyeni nkovu luyanda, nto leyo ebangela intlungu kwi Ngokucofa. Ngu Associated iimpawu zesifo Kawasaki zibandakanya intloko ebuhlungu, umkhuhlane, amalungu abe buhlungu, ukungacoleki kokutya, ekhatshwa iintlungu kunye nokugabha.
Lokufunyaniswa ugqirha ubeka zombini ngokusekelwe iimpawu zonyango, yaye zikhokelwe iziphumo zeemvavanyo nomonde. Ukuba kumanqanaba kwezinga neentlenge erythrocyte, C-izidubuli protein, antitrypsin, transaminases kunye parameters egazini yomguli zikutshoyo kwegazi kunye thrombocytosis, ugqirha aliyi kuthandabuza ekwenzeni unesifo Kawasaki. Esi sifo sizibonakalisa bubukho iiprothini umchamo ubomvu.
Esi sifo kuyingozi ezinokubangela iingxaki intliziyo, kude kube nokwenzeka sisifo sentliziyo, iposi engabalulekanga kunye senyongo. Nomonde kwi urhano nakancinane Kawasaki wathumela uyiqwalasela ukuya cardiologist kunye echocardiography. Xa uhlobo zale sifo, kukho kukukrala imisipha yenhliziyo. Nangona manani, iimeko ezinjalo zinqabile. Kodwa aneurysms kwemithambo yenhliziyo ngokuqhelekileyo ikhula-20% yezigulane. Ukuba ngexesha yokugula kwakhe enokuwona meninges, ukuze aphuhlise aseptic meningitis. Njengoko iingxaki kuvela kumalungu samathambo, kunye ngokoyiswa senyongo - hydrocephalus, ezinobuzaza ziquka eendaba otitis.
Xa yonyango esi sifo okokuqala ezijolise kukhuselo kwenkqubo sentliziyo kunye nokuthintelwa ukusilela kumsebenzi wayo. Isigulane emiselweyo a machiza non-steroidal anti-ukudumba ngeedosi eziphezulu, izithambiso corticosteroid kunye namafutha aqholiweyo. Imihla iintsuku 5-7 ukuya isigulane butofelwe ilawulwa immunoglobulin ukuphucula umzimba kunye ibuyambo ekhawulezileyo malunga nesigulane eso. ezaziwayo-kakuhle ngamachiza zonyango ezifana aspirin enjalo, uyakwazi ukunika uncedo ebaluleke kakhulu kumlo ochasene nesifo ezinqabileyo. Luhlanganisa iipropati eziliqela kwaye isetyenziswa, antipyretic anti-ezithintela ukosuleleka kunye nearhente igazi-hedge. Kwimeko isifo Kawasaki, isetyenziswa nokuba kubantwana abangaphantsi kweminyaka 12. Kutshanje, igazi lweeHedfowuni ukubhitya elawulwa kwizigulane. Ingakumbi isifo ngempumelelo Kawasaki iphathwa ngamaziko zonyango kwaSirayeli, apho izigulane ndenziwa inkqubo plasmapheresis - ucoco plasma yegazi.
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