Yintoni isifo sika-Ollier? Izifo ze-Olia: ukuxilongwa nokunyangwa

Ngaba uziva ukuba umntwana wakho ukhula imilenze okanye iingalo? Mhlawumbi unesifo sika-Ollier. Esi sifo, apho kukho ukungaqhelekanga kokuphuhliswa kwamathambo, oko kukuthi, i-dysplasia yayo. Amanye amagama esi sifo sichazwe ngamathambo amaninzi i-chondromatosis, i-chandromatosis engasetyenziswayo okanye i-bone dyschondroplasia. Igama layo eliphambili lafunyanwa egameni le-oons ohlinzayo olie. Wafumanisa waza wachaza isifo, ngenxa yokusetyenziswa kwe-X-ray, ngo-1899.

Yintoni isifo sika-Ollier?

Esi sifo sibhekisela kwiimpazamo zokuphuhliswa kwamathambo esifo, apho izifo ezininzi zikhona, kubandakanywa oomama abaninzi beintsana ze-hip dysplasia.

Esi sifo sivame ukubonakalisa ebuntwaneni, ngenxa yento eyayicinga ukuba isifo sabantwana. Ngoku kubonakaliswe ukuba ukukhubazeka kunokwenza i-start yayo kubantu abadala (imiqondiso ibonakala nakwi minyaka engama-20-40). Le yintsholongwane yokuzalwa komntwana, kodwa ibonakala kamva ixesha - ekubuntwaneni okanye ebusheni-oko kukuthi, ngexesha lokukhula okukhulu, xa ukukhubazeka kwamathambo kunye / okanye ukuphuhliswa okungavamile kweengalo nemilenze kubonakala.

Ngesifo sika-Olie kwiimetaphyses zamathambo omzimba omzimba weemilenze, i-cartilage outgrowths iyavela. Esi sifo sikhula ngokuyinhloko emathanjeni, emagqabini kunye namaqela ezandla kunye neenyawo, ngokukodwa ezinyaweni nasezandleni, nakwizinthambo ze-pelvic, kodwa kwakhona zivela kwiimbambo, i-sternum okanye i-skull.

I-sprains, okanye i-enchondromas, yenza uhlaka lwangaphandle lwesithambo luqine kwaye lubuhlungu. Enyanisweni, ezi ziimvumi ezinobunzima ezingaba zibi (umz., I-chondrosarcoma). Ngethamsanqa, oku kwenzeka kakhulu kunqabile.

Ngethuba lokuphelelwa komntwana, ukukhula kuzinzile kwaye kuthathelwe indawo ngamathambo.

Ngoko, isifo sika-Ollier-isifo esiyingozi kakhulu, isistim of the squtilaginous skeleton, apho kukho ukunyuka kwama-metaphyses (amathambo omzimba wesibeletho). Isizathu sokwenzeka kwayo asikaziwa. Kwimizekelo yamatyala, inomlinganiselo ophezulu wezityalo zofuzo.

Efana ne-dyschondroplasia, izifo ziNqabucci ezinqabileyo kunye namaProteus syndromes. Ekuqaleni, ngaphezu kwezinto ezinobungozi kunye nezidumbu ze-skeletal, i-hemangiomas yenziwe kwibala-bomvu indawo enokungafaniyo, enemizila yegazi. Kwesibili, izicubu ezinobunzima zikhula kwiindawo ezahlukeneyo zomzimba.

Ngubani ochaphazelekayo sisifo

Ekuqaleni kwakukholelwa ukuba i-chondromatosis yamathambo ayiqhelekanga. Kodwa ngoku, xa uphando lwe-X-ray luqhutyelwa ngokubanzi, kwavela ukuba ayikwazi ukubizwa ngokuba yi-rarity. Ukuba iminyaka engama-20 edlulileyo, iimeko ezingama-30 zachazwa, ngoku ziphindwe kabini.

Ngokuqhelekileyo akunakwenzeka ukucacisa ukuqala ngokuthe ngqo ukuba ukuhlolwa kwe-X-ray okuthe rhoqo akuzange kwenziwe ukususela ekuzalweni, ingakumbi ebuntwaneni kunye nokuphuhliswa kwe-intrauterine, xa, ngokuqinisekileyo, isifo sika-Olie sivela. Esi sifo, ngokusoloko, kumantombazana sitholakala phantse kabini ngokufana nakumakhwenkwe.

Iimpawu zesifo

Ukuze bangaphuthelwa iimpawu zesi sifo, abazali kufuneka baxelelwe ukuba umntwana:

• Ezinye izicwangciso / izitho zomlenze zilibazisekile ekuphuhliseni;
• Kukhona i-asymmetry kunye nokunciphisa kuzo;
• I-Lameness ibonwa;
• Kukho i-skew ye-pelvis;
• Kukho iikrubvity of joints in the valgus or type varus.

Zonke ezi zinto zenza kube lula ukuba umntwana unesifo sika-Ollier.

Esi sifo asibonakali ngaso sonke isikhathi ngokuzalwa, kodwa sele sele sele uneminyaka engama-1-4 ubudala unokubona ukuba imilenze yomntwana okanye izandla zikhula ngokukhawuleza kunokuba zikulindeleke. Esi sisona sibonakaliso esibalulekileyo sesi sifo, esingenakukunyanzelwa. Kulo lonke, umntwana uyaqhubeka ngokuqhelekileyo, nangona efunyenwe ukuba "u-Olie's disease".

I-Dischondroplasia ihlala ichaphazela isinye isigxina, nangona kunjalo, iimeko zokutshatyalaliswa kokubili aziqhelekanga. Ukuba isifo sithinte imilenze, umntwana uya kuba nokukhula okuphantsi ngenxa yokunciphisa. Ngokukodwa ngokukhawuleza ukulahla emva kokukhula kwethambo, ukuba inkqubo ye-pathological iqala kakhulu kakhulu. Ukuguqulwa kukubuhlungu, inkqubela phambili. Ukuphelela, phantsi kwesi sifo, kuba ngumncinci, utyhafile, utshintsho oluthile, ukugqithisa ukuphawula. Kukho i-varus okanye i- valgus deformity yamadolo (ubuncinci becala - ukuphela kokukhawuleza kwethanga okanye unyawo), i-scoliosis yomgudu. I-muscular atrophy nesi sifo asikho.

I-phalanges, i-metatarsal kwaye, kwezinye iimeko, amathambo e-metacarpal alawulwa utshintsho olukhulu. Zifutshane, zandiswe, ziqine kwaye ziqulethe izikhanyiso ezininzi.

Abo babandezelekayo esi sifo baxhomekeke kwiintlobo, njengoko izicubu zethambo zikhula ngokungalunganga ngenxa yesifo. Nangona kunjalo, iziqhekeza zivame ukukhula zihamba.

Izifo ezihambelanayo

I-Dischondroplasia inokuthi ihambisane nomonakalo kwamanye amalungu, nangona izifo ezithintekayo azihlali zikhula. Ngokukodwa, kumantombazana amancinane, kunye nesifo sika-Olie, i- ovarian teratoma kunye neengxaki ze-endocrine ziyakubonwa, kubandakanywa ezinzima, kubandakanywa nokuhamba kwimihla yokuqala kunye nokunyuka kwexesha elide ngaphambi kokunyuka kwe-ossification.

Nangona kunjalo, uphuhliso lubuyela kwindawo eqhelekileyo ngokususwa kwe-tumor ye-ovari.

Diagnostics

Ukuchonga isifo se-Olie, okokuqala kukho konke kufuneka wenze i-x-ray. Kufuneka kwenziwe i-bone biopsy kunye ne-magnetic resonance imaging. Ukuba isifo sifumaneka, izigulana zifuna ukuhlolwa rhoqo ngogqirha, ukuze kufike ngexesha elifanelekileyo ukuchazela utshintsho olubi kwi-chondrosarcoma, ukuba kuyimfuneko.

Ukuxilongwa ngokubanzi

Ukuxilongwa ngokwahlukileyo kwisifo se-Olie, eqinisweni, ayifuni emva kokuhlolwa kwe- X-ray, njengoko umfanekiso we-chondromatosis uchanekile. Nangona kunjalo, nganye imeko iyimfuneko, kwaye isethi yempawu ezibuhlungu ayinakuphindaphinda, ngoko ke oogqirha kufuneka bangabandakanyi izifo ezifanayo.

I-X-ray ingabandakanyi i-chondrodystrophy ye-atypical, i-hemygypertrophy okanye i-hemiatrophy bone, i-rachitic deformities nezinye izifo. Kwakhona, ngenxa yemifanekiso ye-X-ray, isifo sikaRecklinghausen asifakiwe, esingaqhelekanga sidideke nesifo se-Olie. Umgaqo oyintloko kukuba wenze i-x-ray ye-skeleton yonke, kungekhona inxalenye yayo.

Iimigaqo zonyango

Dischondroplasia ngoku, ngelishwa, ayinayo iindlela zokwenza unyango olunengqiqo. Ngokwahlukileyo, umzekelo, kwisifo esifana ne-hip dysplasia, i-chondromatosis iphathwa kuphela ngokulungiswa kokuchithwa kwe-deformation. Kwezinye iimeko, i-endoprosthetics yokufakelwa ibonisiwe. Olunye unyango olufunekayo isiguli luyimpawu kwaye luxhasa.

Ingenelelo yokuphanda ibonakaliswe ikakhulu kubantu abadala, njengoko, ngokubhekiselele kwimihla ngemihla, ukulungiswa okuzinzileyo kwiminyaka yesikolo, iziphumo ezizinzile azifumanekanga, oko kuthetha ukuba umlinganiselo wokwenza unyango otyunjelwe kuphela ngokutshabalalisa okwenziwe, kodwa kungenjalo. Nangona kunjalo, ngezilonda ezinzima, ukungenelela okuphandle kunokwenzeka nakwizibantwana, ngakumbi xa kuziwa kwiminwe ephosakeleyo kakhulu kwimeko yesifo sika-Ollier.

Esi sifo sifuna ukugcinwa kwamalungu kunye namathambo: izigulane ziboniswa zimbethe izicathulo zomzimba, zisebenzisa i-orthopedic idivayisi kunye nezinye izixhobo ukuzinzisa izihlanganisi. Izigulane kufuneka zibandakanyeke kwimigqaliselo eyenzelwe ngokukodwa le ngxaki yokugula kunye nezemidlalo eziyinkimbinkimbi.

Ukuzivocavoca okuncedisayo kunye ne-gymnastics kunye nokuzivocavoca kwiimimulator ezikhethekileyo. Oku kunceda ukubuyisela ithoni ye-muscle nokuqinisa ii-ligaments.

Forecast

Ngokomphando, ngokuqhelekileyo ukunyuka kwamathambo e- oldti cartilage kuthatha indawo yetshe (mhlawumbi, kungenxa yabantu abadala, iimeko zesifo ziqabile kakhulu). Nangona kunjalo, kubantwana abancinci, ukugxekwa akukhuthazi kakhulu: ukuguquka, nangona kunjalo, kodwa ihamba phambili. Yiyo kanye oko isifo sika-Ollier sisingozi.

Esi sifo sibonakaliswa ngabanye kwimeko nganye, ukuba kuyo yonke ingqungquthela ibinzima ukuqikelela. Ngezilonda ezininzi, kulunge ngakumbi kunokuba kukho imeko eguqukileyo yendawo. Ukuqhaqhaqhaqhaqhaqhaqha kubangela ukunciphisa enye yeengalo kunye, ngoko ke, kwi-asymmetry yabo, ingakumbi xa kuvela kubantwana abancinci. Kwaye akunakwenzeka ukulungisa. Kwakhona, ukuphuhliswa kokuqala kwamathumba kunyusela umngcipheko weendlela ezahlukileyo zeminwe.

Ukuguquka kwi-chondrosarcoma

Nangona into yokuba utshintsho kwifomu elibi - i-chondrosarcoma - livela ngokungapheliyo, kusekho nethuba lomhlaza. Oku kuninzi oku kwenzekayo ebusheni, nangona uphando lwezifundo zanamhlanje lubonisa ukuba oku kuya kwenzeka kamva. Ngenxa yoko, izigulane ezine-dyskondroplasia zicetyiswa rhoqo kunye nogqirha kunye neemviwo zonyango.