Isifo seLennox Gasto (isithuthwane)

I-Lennox-Gastaut syndrome yenye yeendlela zokuhluthwa (i-myoclonic-astatic). Olu hlobo lwesifo lubonisa ukudibanisa kwe-toniki kunye ne-atonic, i-absypical absence, ukuphuza ukuphuculwa kwengqondo kubantwana. Ngesihlandlo sokuqala eso sifo sinokuthi senzeke kwiintsana ezincinane ukusuka kunyaka ukuya kwiihlanu, ikakhulukazi kubafana.

Esi sifo, njengomyalo, siphumela ngenxa yezifo zengqondo ezidluliselwe ebuntwaneni kwaye ziqala ngokuwa ngokukhawuleza komntwana. Emva kwexesha kukho ukudibanisa, ukuxhamla, ukunyamezela ukuphuhliswa kwengqondo, kunye nokuhla kweengqondo.

Ngokuthe ngcembe, ngokukhula komntwana, uhlobo lokuthintela luyahluka. Amaposkitha athatyathwa yinto ekhethiweyo, isistim yesibili, ukuhlaselwa ngokukrakra kokuthwala.

Ngenxa yento eyenziwa yi-Lennox-Gastaut syndrome

Kunzima ukuqonda iimbangela zalesi sifo, kodwa namhlanje ezi zizona zizona ziyaziwayo.

• Anomaly ekuphuhliseni ubuchopho.
• Izifo ezithintekayo (i-meningitis, i-encephalitis, i-rubella).
• Izifo zesifo se-genetic zesifo sengqondo (i-CNS izilonda, izifo zesifo, isifo se-sclerosis).
• Ukulimala komntwana ngexesha lokungena kwinqanawa yokuzalwa (i-asphyxia, ukuzalwa kwangaphambili, njl.).
• Utshutshiso lwe-CNS ngexesha lokubeleka kwangaphambili, kunye nokuzalwa kwangaphambi kokuzalwa kunye ne-asphyxia.

Iimpawu zeSLH

Isifo seLennox-Gastaut sinokuqatshelwa ngumbonakalo obaluleke kakhulu - ukuxubusha. Abantwana abafumene ukuba ne-idiopathic epilepsy baneendlela ezahlukeneyo zokuhluthwa (iimpawu) :

• Iiparoxysms zokuwa;
• I-Atonic inxinzelelo;
• Ukungabikho kwamanye amazwe;
• Ukuxhatshazwa ngokukodwa;
• Iikrampu zendoda;
• Ukukhwabanisa kweMyoclonic-astatic;
• Ukutshatyalaliswa kweT Tonic (ngokuqhelekileyo kwenzeka ngexesha lokulala ubuthongo obunzima);
• I-TC iyakubamba.

Izigulane kunye ne-Lennox-Gastaut syndrome nazo zinomdla wokutshintsha ngokukhawuleza ekuthinzeni, ukuphuza kwengqondo, ukuphazamiseka kwengqondo, ukuphazamiseka kwengqondo kunye nobuntu.

Ukuxilongwa kwe-LH syndrome

Ngokukhawuleza emva kokubonakalisa isibonakaliso sokuqala kwesi sifo kubalulekile ukuba ufune uncedo ngokukhawuleza kwiingcali, ubiza i-ambulensi. Njengomthetho, ukuxilongwa kwesi sifo kwenziwa nge-ECG ngexesha eliphakathi kokuhlaselwa.

Unyango lwe-LH syndrome

Isifo seLennox-Gastaut siphathwa ngoncedo lwezonyango kunye neendlela zokucoca. Unyango kunye namachiza uvelisa umphumo omuhle kungabi ngaphezu kwe-20% yamatyala. Ngendlela yokugonywa kwonyango, ukuphelisa ukuwa ngokukhawuleza, ukusebenza ngokufanelekileyo kukusasazeka komzimba okhuniweyo (kallozotomy). Kwakhona, imisebenzi ejoliswe ekuvuseleleni i-nerus nerus kunye nokususa izicubu ze-vascular kunye neentsholongwane zisetyenziswa.

Nangona kunjalo, kufuneka kuthethwe ukuba ukuxhatshazwa kweziganeko ze-syndrome kunzima ukunyanga; Ekugqibeleni banokubangela isigulane kwimiphumo enzulu yentlalo kunye nengqondo. Ukubanjelwa kwe-Tonic ekhokelela ekunciphiseni kweengcaphephe akunakwenzeka.