Zempilo, Diseases and nemibandela
Pancytopenia - imeko zophendlo lwezifo apho awusafuni kwi elijikeleza egazini zoonke nokwakheka. Oonobangela, iimpawu, unyango
Naluphi na uphuhliso sifo umzimba ibangela utshintsho yokusebenza egazini peripheral. Nakuba kunjalo, kukho iqela ezimbi apho shintsho iphambili lwezonyango. Pancytopenia - yenye yeenkqubo zophendlo lwezifo kwenkqubo hematopoietic, echazwe njenge sifo ezimeleyo, okanye inokuba njengokubonisa kwezinye ezihamba nosological.
imiba ngokubanzi
Esi sifo akuxhaphakanga, ngoko abantu abaninzi abangayaziyo into enjalo. Pancytopenia - imo ukuswela egazi, uphuhliso nto leyo ebangelwa ezingaqhelekanga xa isakhiwo iiseli precursor xa ibakala hematopoiesis. Amanqanaba Ukuncipha iiseli ezibomvu, iiseli ezimhlophe zegazi neeplatelets ngenxa yokuba iiseli stem akakwazi ukusebenza ngokwaneleyo.
Esi sifo senzeka ngeendlela ezimbini:
- idiopathic, okubangelwa zizinto zangaphakathi;
- aphakamileyo, nto leyo ibangwa mpembelelo zangaphandle.
Umqathango yezifo nowama-50% amatyala iphuhlisa uhlobo sokuhlasela. Oko kukuthi, umzimba ukulwa yedwa iiseli zakho igazi, iphambanisa nabo arhente zasemzini. ifomu Idiopathic kuvela njani nxamnye kuthinjwe into ezongezelelweyo lwangaphandle oluya ibalekisa isiphumo esibi.
Pancytopenia - sisifo yimfuzo, ekuphuhliseni kwixesha xa usana esibelekweni. Umntwana ozelwe sele nokuphazamiseka igazi-forming amalungu. Kunokuba iziphene kunye lomongo wethambo hypoplasia, ukuze le nkqubo abakwazi ukumelana nemisebenzi yazo.
I-umyalezo we wemiba sifo kunye nobungozi
Phakathi Iimbangi ezingundoqo kuphuhliso zezifo kwiDNA, ukusetyenziswa ixesha elide kwamachiza, ezinemitha okanye iziphumo ezinetyhefu. Noko ke, uhlobo Idiopathic luphawulwa kukuba azinako ukusekwa unobangela, kwakukho amatyala esi sifo emva yokuzala.
Ukumiselwa izizathu, kubalulekile ukuba ayaphumelela. Ekuyekisweni nempembelelo lwangaphandle zingafanelekanga sifo - 50% lomlimganiselo wempumelelo.
Ukongeza izizathu eziphambili kukho izinto ezininzi ukuba negalelo kuphuhliso emoyeni:
- Sebenza benzene okanye esiyityhefu;
- igazi Fanconi;
- uhlobo wentsholongwane egazini zokosuleleka;
- chemotherapy;
- elwa immunosuppressants;
- izifo komzimba ezifana systemic lupus zomzimba;
- radiotherapy.
igazi Fanconi - enye yezona zinto etiological of pancytopenia. Phuhlisa kwisiqalo mgceni iziphene kugqalwa unesifo autosomal sofuzo. Anaemia luphawulwa ubukho iziphene iinxenye iiprotheni anoxanduva DNA yokulungisa kunye chromosome friability.
Lo mfanekiso kwezonyango sifo
imeko yezifo esizibonakalisa ngokohlobo syndromes ezintathu. Nganye kwezi mpawu Uphawu ukunciphisa inani elinye uhlobo kwiiseli. Leukopenia iboniswa umfanekiso nokudumba acute kunye ukuvela iinkqubo isilonda-necrotic ulusu kunye ngenwebu yangaphakathi.
Erythropenia kunye nokwehla ukuziphawula ngehemoglobin nimqumbise uphuhliso iimpawu kwegazi. Le meko lubonakala:
- isiyezi yesikhumba integument;
- izibawu phambi kwamehlo akhe ;
- nesiyezi;
- ukuduma;
- ubuthathaka nokudinwa;
- ubuthathaka.
Izigulane ezikhala ukuphelelwa umoya kunye nentliziyo iyangongoza. Auscultation ukumisela neethowuni ngentliziyo qegu, nisikrokrele iSystolic kulo lonke kumphezulu ngeprojektha kwentliziyo, nesandi phezulu ndlela jugular. Eziya zisiba mbi imeko yomguli ibangela utshintsho kwi electrocardiogram, abonisa uphuhliso ukusilela kwentliziyo.
Thrombocytopenia kuboniswa rhoqo ukopha (epistaxis, emathunjini, zesibeleko), ukopha iintsini, imbonakalo petechiae kunye hemorrhages esikhumbeni. Iimpawu zale sifo zigcinwa malunga ngenyanga yaye ngokufuthi kukhokelela ekufeni. pancytopenia Chronic wavumela elilungileyo ngakumbi kwaye iimpawu ngaphantsi ucaca
esi sifo ithathwa kuba entsonkothileyo kakhulu. Pancytopenia, leyo ezinobuzaza zixhaphakile kakhulu kubantu abadala, sikhatshwe inkangeleko zizifo kunye ukopha.
amanyathelo zokuxilonga
Kwimeko yokuqala ifuna ukuthunyelwa ukuhlolwa specialist, imbali ukuqokelelwa kunye nobomi isigulane. Ngaphezu koko wamisa ICBC. Kwimeko ezi zalathisi banokucamngca kuphuhliso pancytopenia kwaye baqhube amanyathelo diagnostic:
- leukocytes <2 x 109 / l;
- zegazi <150 x 109 / L;
- erythrocytes <3,5 x 109 / l.
Babelwa ukufunda lomongo wethambo okuhlatywa, nto leyo ichaza ukuba ubukho iiseli ezingaqhelekanga kunye myelokaryocytes. Ikhethwa bubukho ezingaqhelekanga, kuquka lomongo wethambo hypoplasia. Kwakhona kubanjwa iisampuli hemolytic.
unyango pancytopenia
amanyathelo therapeutic kuxhomekeka kwimeko lwezonyango, imeko yomguli kunye factor etiological ezibangele ukuba isifo. ingasetyenziswa Ezi ndlela zilandelayo unyango:
- Igazi, ukuba ukulungelelanisa intsalela uhlobo lweziqalelo.
- Abohlukeneyo ezinomongo yethambo okanye esiqwini iiseli. Kudla lwenziwa izigulane yobudala abatsha ophakathi.
- Kwimeko pancytopenia samathambo ezilawulwa isicelo immunosuppressant "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
- Kuthetha zivuse umongo ukusebenza - "Neupogen", "Neulasta", "Procrit", "Leukin".
izityalo zamachiza
Uthomalaliso sifo esimbaxa kuquka ukusetyenziswa namakhambi. Inqanaba iiseli ezibomvu futhi umthamo banokuvuselwa ngoncedo amaqunube. iti enqatyisiweyo zenziwa ngokusekelwe uthuthu, currants abamnyama, wavuka iinyonga, amaqunube, namaqunube, apricot. Ayina theniphu sisityebi, gooseberries, cherries kunye iidiliya, ukudla zazingathandanga balance kuphela intsalela egazi, kodwa ukomeleza amajoni omzimba.
Iqela iindlela intsomi ngokuphatha pancytopenia iquka nobusi. Oku kuhlanganiswa kunye neemveliso zilandelayo:
- kunye newayini elibomvu kunye zekhala;
- garlic;
- oats;
- lemon, nezo ziqwayitiweyo, zeerasintyisi, uyawathena kunye walnuts.
Qhoboshela kubaluleke kakhulu infusions kunye decoctions womfuno amayeza ziya kumila into umba, ezinde, umyalezo ingca, i-, edandelion, orchid, i-, buckwheat.
isiphelo
Pancytopenia - bagula kakhulu, nto leyo kulingana isifo esibulalayo. ayaphumelela kuxhomekeke ubungqongqo iimpawu zonyango, iintlobo kunye zokukhula oqale unyango. sifo kulula ukunqanda kunokuba elapha.
Iimviwo lonyango yonyaka abantu kunegalelo ekuchongweni imeko zophendlo lwezifo kwi usaqala. Ingakumbi oku kusebenza iindlela iimviwo elebhu.
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