West syndrome

Kuba ngqa inkantsi engaqhelekanga bobusana ezichazwe West kwi 1841st. Ngoko ke umbuzo yonyana wakhe. Ingakumbi wagxininisa ngokuqhubekayo inkqubela iimpawu lengqondo in. Isifo kubhekwa esinganyangekiyo.

West syndrome kwakukho iimpawu triad uphawu - series ophindaphindayo inkantsi, lengqondo abazizidalwa, utshintsho express (paroxysmal) kwi EEG. Qala ngokuthe ngcembe, iimpawu yokuqala naxa abantwana abasempilweni kungenziwa kakuhle ngaphambili, nangona ngokuqhelekileyo kubonwe imvelaphi obukhulu lengqondo ukulibaziseka. Ivame kakhulu kubantwana iinyanga ezine ukuya kwezintandathu, kodwa kusenokwenzeka isifo kamva (ukuya kwiminyaka emine). Boys baboniswa sifo ngakumbi.

aqaqambayo bobusana ngokuqhelekileyo macala, amabini, elifutshane, kunye yindibanisela ngesiquphe amaqela kwezihlunu. Ukuhlaselwa Character kuxhomekeke amaqela athatha inxaxheba kwinkqubo (flexor, extensor). Amahlaba zingasasazwa nokuba zonke izihlunu okanye umntu (izihlunu entanyeni, izihlunu ka esisu). Eziqhele ukufunyanwa aqaqambayo engumxube, kulandele ukwanda - flexor, nokuba anqabe - le extensor. Ngaphezu koko, kukho spasm kuxhomekeka kwindawo ethile yomzimba.

West syndrome badla ingqalelo inkantsi kanye flexor. Ukuba inxaxheba esiswini izihlunu-ukugoba, umzimba ukwazi ngokubanzi isongwe kwisiqingatha. Xa u ezisekupheleni eliphezulu, iintshukumo ngesandla iyenziwa zokuphambukisa-kungeniswe (kubonakala ukuba umntwana ngokwakhe iqala ukuba bamkele). Kunye nokubandakanyeka izihlunu flexor entanyeni ingena ngathi bevuma. Ukuba kwizihlunu inxaxheba ze umbhinqo umkhono, umntwana njengoko akayihoyi le nto. Aqaqambayo kunganqanda iintshukumo nistagmoidnymi okanye kuxhuzula kwezi lweliso lakho. ukusilela kunokwenzeka kunye zokuphefumla. Esi sisihlandlo sokuqala iimpawu ukuxhuzula.

Uhlobo ziba le umyalezo akuxhomekekanga, njengoko awuvumeli ukuqikelela uphuhliso sifo. Nangona kunjalo, indima edlalwe yi ubukho macala (asymmetry ibonisa sisilonda esidumbileyoesingaphakathi cortical). aqaqambayo yezi bazimisele, umzekelo, amehlo osisi-ukhokelo okanye intloko.

Aqaqambayo ngokuqhelekileyo kwenzeka xa ndivuka okanye ukuwa umntwana elele. Ngaphantsi nje therebetween imizuzu lekhefu. Ukunyuka ngamandla, koko kunciphisa. frequency ezahlukeneyo - ukusuka inkantsi abangabodwa ukuba amakhulu ngosuku. Baya ezinokubangelwa ingxolo okanye ephathekayo.

Emva ezayo amahlaba kuncitshiswa reactivity. Abantwana sele khona mna, aninako awe (yokuyeka nokuhlaselwa).

West syndrome kucingwa ukuba uhlobo lixhaphakileyo Encephalopathy unesathuthwane, ekhokelela Ukuphazamiseka kwengqondo. Kuthintelo Akukho data.

West syndrome kwenzeka ngenxa yezizathu ezahlukeneyo. Zizalwa - i ixhaphakileyo. Ukongeza, isenokuba ezingaqhelekanga, naso zobuchopho, Ukopha intracranial, njalo njalo. Ngamanye amaxesha unobangela sifo zingenakuqinisekiswa.

Ukuba usana lwakho West syndrome, unyango iqala ngoko nangoko. Nawe amisele unyango lwezempilo, kwaye kunokwenzeka ukuba longenelelo efunekayo, yaye oogqirha abo ukususa iziko lwezidumbu, ebekwe kwenye indawo kwi ebuchotsheni. Yeha, ithuba lokuba ufumane eli ziko ayisoloko kwenzeka, kwaye kwezinye iimeko, kwanaxa elibhaqiweyo, akunakwenzeka ukuba ukucima.

Ukuba iyeza kufuneka kwenzekile ikhosi kwamkela, iziyobisi antiepileptic ngamnye ekhethiweyo ezizodwa. Kumiwe ukuxhuzula ndiqononondise kwimpumelelo unyango, Noko ke, unyango kufuneka linatyiswe ukuze elinesihlanu (kwaye ubuncinane) kwiinyanga. ulwazi lwezonyango lubonisa uyekelelo kubakho esi sifo-60% abantwana, ukuhlasela eseleyo, ngelishwa, ukuba zihlaziywe.

oogqirha bakwaSirayeli bathi, izifo kunye nefom cryptogenic ALS kungcono kakhulu. Ngokunzulu care ukuhlaselwa shot, umntwana "basoyise" syndrome, ukulibaziseka yophuhliso ilungiswa imidlalo kwezemfundo. Xa uhlobo kwangumqondiso abane isikroba. Ukuba siyakwazi ukutsala ekuhlaselweni ukutshayela umthombo kuqala sifo (malformation, nangezilonda, cysts), ukuhlomela uMthetho odi asahleli ephezulu.