Zempilo, Diseases and nemibandela
Ondine Syndrome: Oonobangela, inkcazelo, unyango
Ondine syndrome - kangaka ngokuba oogqirha hluleka ngamaxesha athile ukuphefumla, nto leyo ibonakala kokubini kwiintsana kunye nabantu abadala. Kubonakala, kutheni?
Kutheni ibizwa?
igama layo, Ondine syndrome kwakubangelwa komnye amavo endala. Ngokutsho kwakhe, umnini Ringshtetten Castle - Knight Guldbrandt - yalahleka emahlathini damn. Ekufeni kusindiswa ngaye umlobi omdala, ukunika indawo yokufihla endlwini yakhe. Kwaba khona ukuba knight amanene, yaye wamthanda kunye sikamamlambo ongafiyo Undine - ntombi endala awuqeshelweyo. Undine kwakhona wayethanda Guldbrandt, waza wavuma ukuba abe ngumfazi wakhe, wosithwala umntwana wakhe. intombi-ntlanzi yasentsomini Immortal emva kokuzalwa, unyana wakhe ijikwe ibe ngumfazi ofayo. sele kudlule iminyaka emininzi, iminyaka yachithwa Ondine yangaphambili ubuhle waza wathabatha uthando nomyeni wakhe. Xa Ondine ebona umyeni wakhe Iingalo inenekazi eliselula - Bertaldy. Kwenzeka ntoni emva koko, ilivo ayicacisi - nokuba Ondine antywiliselwe iDanube ngokwayo, okanye kule wasiza umyeni wakhe, ephosa esiphelweni. Kodwa Guldbrandta, kungekudala bagqiba ekubeni atshate i Bertalde oselula, elindele ukuba ubomi elingcangcazelisayo; wayebonakele kuye, uMoya ka Ondine isiqalekiso umngcatshi perfidious, kwanyanzeleka ukuba ugcine engqondweni, nokuba ebusuku, ukuba kuphefumlwa njani. Ngokuba kuye, iphupha waba ebulalayo, ngenxa yokuba, nokulala, akayi kuba nako ukulawula ophefumla ngayo baza bafa.
Namhlanje Ondine syndrome - igama sesikweni yomsebenzi stop nokuphefumla ngexesha ubuthongo.
kwenzeka ntoni?
Igama laso esemthethweni isifo - ". belele" Lubonakaliswa notyeshelo imisebenzi iziko bokuphefumla zokumisa xa ulele, ukuphefumla. Ukuba aveze, isifo unakho ebuntwaneni, kwaye naliphi na ixesha ubomi babantu. ezichazwe krelekrele ngayo kwixesha lokuqala umntu owakha wambona isiqalekiso Ondine syndrome, Wisniewski - umbhali Polish ethandwayo (yingqokelela yamabali amafutshane "iNkosikazi").
Xa isigulane iyolala, ngoko, ngenxa yaso nasiphi na isizathu, umzimba wakhe akuthethi ukwenza umsebenzi oluzenzekelayo onommiselo ukuphefumla, nto leyo esisizathu sokuba umntu akanako ukuphefumla ngokuzimeleyo, kwaye ngenxa yoko, into ukomiwa apho, okanye njengoko ibizwa ngokuba amagqirha - disritmicheskaya hypoventilation. Kulapho kwezo zihlandlo, ngokuphawulekayo kunciphise inqanaba ioksijini angena umzimba, ngenxa leyo elinganeno umsebenzi kwiindlela ezininzi omzimba, kubandakanya ingqondo.
Ngubani bachatshazelwa sesi sifo?
Ngokungafaniyo nezinye izifo ezichaphazela becala ethile ubudala okanye isini iqela labantu phantse na ubudala ngazo isiqalekiso Ondine syndrome. Xa abadala, ngokwenene inqabile kakhulu kwaye ikakhulu saphawula kwiintsana kunye nabantwana.
Kwenzeka ntoni emzimbeni?
Njengeempembelelo emzimbeni womntu nesiqalekiso Ondine syndrome - belele? Okokuqala, kukho ukwehla inqanaba ioksijini egazini, abaphethwe inkqubo Cardio nemithambo. umsipha wentliziyo uqala ukwehla ubomi, iimpahla zixinaniswe kakhulu, ngaloo ndlela zokukhulisa uxinzelelo lwegazi. Xa kwasebuncinaneni bakhe, xa umntu isekhona ngokupheleleyo amandla kunye nomzimba ayibhuqwanga yi izigulo ezahlukahlukeneyo, zonke ezi zinto azithathelwa ngqalelo. Ndakuva ubudala nangaphezulu, xa umzimba sele kakhulu "kunxitywe" ezifana xi ubusuku ngokulula zivuse ukufa icala okanye intliziyo ukuhlasela, kwaye kukhokelela ekufeni.
Iintlobo elele
Ondine syndrome - kukwaphula umsebenzi nokuphefumla ngexesha ubuthongo kuphela. Oogqirha bahlule nezinye iintlobo elele:
- neuropathy (obstructive);
- central;
- mixed.
belele neuropathy luphawulwa rhoqo, amatyala angaphezu kwe-15 ngeyure, eyeka umsebenzi yokuphefumla, ogama ubude idlula imizuzwana 10. Nale hlobo intshukumo umoya komoya iyakuvingca kwi yomoya eliphezulu, ngenxa apho umoya na bephefumla kungena emiphungeni. Ngokuqhelekileyo, ezifana ukusilela sokuphefumla kwenzeka ngenxa ephula sicatshulwa neemvakalelo luvo ukuya pharyngeal kunye nezihlunu zemiphunga.
belele Central kwenzeka ngenxa yokuba yomoya abafumani ubume isebenze eyimfuneko evela kwinkqubo luvo (CNS). Ukuphuhlisa imeko enjalo, ngokuqhelekileyo ngenxa yeenguqu zophendlo lwezifo kakhulu kubume ingqondo, ngenxa emphefumlweni okanye izifo.
Iimpawu zazo zombini apneas neuropathy central waphawula kokubizwa-uhlobo engumxube, elithanda olufunyanwa neonates kunye neentsana.
iimpawu
Ngenxa izifo ezifana belele (nokuba peripheral, central okanye uhlobo mixed), kukho rhoqo zombini abazi nokuba umnxeba zingqondweni, ukutshintsha uhlobo nokusebenza imithambo sentliziyo kunye negazi. Konke oku kukhokelela kuphuhliso mpawu zilandelayo:
- ngosuku:
- fatigue eliphezulu;
- imvakalelo rhoqo ukukhathala nokungabi namandla;
- ikhanda kusasa;
- ukukwazi ukuzikisa memory kwanciphisa;
- ukungazinzi ngokweemvakalelo.
- ebusuku:
- iingxaki ndilale and ugwayi;
- Awakening rhoqo;
- ukubila;
- echama rhoqo.
Ukongeza kwezi mpawu, njengoko umonakalo namanye amalungu kunye neenkqubo, apho kuya kubakho imiqondiso ezintsha yokuphazamiseka kwimisebenzi zomzimba.
ongenabuntu
Kude kube kwisiqingatha sesibini senkulungwane yokugqibela, izazinzulu ayikwazanga bana phandle into ebangela oko isiqalekiso Ondine syndrome, izinto yayo zazicacile kwaye twisisaka. Akukho namnye unako ukuphendula umbuzo wokuba kutheni iintsana uphilile namakhwenkwe, amadoda kunye nabafazi ngesiquphe wafa ebuthongweni bakhe ukusilela sokuphefumla. Kuphela ekuqaleni-imi- 60 kwinkulungwane XX, abaphandi R. Mitchell kunye George. Sevringausu kwafunyaniswa ukuba esi sifo luhlobo elele. Le lokufumanisa wanceda izazinzulu ukwenza isigulane ophelelwe ulawulo oluzenzekelayo lokuphefumla ngenxa yomonakalo engqondweni. Njengoko kwakunye izigulane kunye syndrome Ondine, ixabiso kwisigulana zilale, ukuba iliso njani umsebenzi yokuphefumla, wayengenakukwazi, ibe ngenxa yoko laqalisa yayiminxa. Noko ke, ezi zifundo abazange babe nako ukuphendula umbuzo wokuba yintoni ebangela aba ukuphazamiseka ngabantu abaqhelekileyo.
Kuphela kwinkulungwane xxi abaphandi French baye bakwazi ukuseka unobangela kwesi sifo. Esebenzisa uthotho amalinge, ke oosonzululwazi bafumanisa ukuba ngokusilela yokuphefumla kwizilwanyana unoxanduva Thox2B sofuzo. vo isampula Further sabantu ukusuka syndrome Ondine, waqinisekisa ubukho isakhi enye, yaye. Enye isiphumo ebalulekileyo kukuba guquko gene ayikho ilifa kwenzeka ngexesha kuphuhliso osandul.
nesiqalekiso Ondine syndrome: Treatment
Kangangexesha elide, ngaphandle kokuba uxhulumaniso abantu abagulayo ebusuku ukulawula umatshini ukuphefumla, uyakwazi ukumelana sifo wayengekho. Kwiminyaka embalwa edlulileyo kumazwe aliqela aseYurophu, ezifana Sweden, Germany kunye nabanye, baye ingenisa ebuchotsheni, ngokukodwa luvo phrenic, izigulane kunye syndrome Ondine izixhobo ezizodwa, apho "ziquka" impefumlo xa wayeka. Ngokutsho kokuma izigulane esisebenza, naziphi na iingxaki kunye uphefumla ebusuku, yaye apho zingasekho lokuzibona emini.
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