ZempiloDiseases and nemibandela

Iimpawu kunye nonyango lwe antiphospholipid syndrome

Phantsi sifo antiphospholipid amayeza ibhekisa kuphazamiseka apho amajoni omzimba ngempazamo ukhupha izilwa sibhekiswe ezinye iiproteni igazi yesiqhelo. Le meko ke Usenokuziva ukuyilwa amahlwili egazi kunye neengxaki ngethuba lokukhulelwa (kwesisu, ifile, njalo njalo). Kweli nqaku siza kuthetha iimpawu eziphambili le ngxaki, kwaye cinga ukuba yintoni na unyango antiphospholipid syndrome.

Izizathu

Njengoko sele kukhankanyiwe ngentla apha, kweli syndrome ngokwayo kuchaphazela iiproteni amajoni omzimba ukuba ubophe phospholipids (amafutha ukuba zifumaneka igazi kwaye zibalulekile amahlwili eqhelekileyo kuyo). Okwangoku, iingcali kwemiqathango ukwahlukanisa iindlela ezimbini iingxaki:

  • izifo ezibangelwa okanye izifo ezithile (umz, i-HIV, isifo seengcongconi, hepatitis C, njl) - Primary School.
  • Uhlobo secondary ngokuqhelekileyo sibonakala izigulane abaye ngaphambili kwafunyaniswa naziphi na izifo sokuhlasela. Ngoko ke, kulo mzekelo, uphuhliso antiphospholipid syndrome inokuba kunokubangelwa disorder ephambili sokuhlasela.

iimpawu

Namhlanje, iingcali ziye zachongwa eziliqela iimpawu uphawu antiphospholipid syndrome. Zidweliswe apha ngezantsi nje ezinye zazo:

  • ukuyilwa egazi igazi ngemithambo imilenze;
  • ifile, kwesisu rhoqo okanye ezinye iingxaki ukukhulelwa;
  • ngesibetho;
  • ebuhlungu rhoqo, amahlaba;
  • irhashalala eluswini ngohlobo lwe-grid;
  • isifo sentliziyo ;
  • ukopha.

syndrome Antiphospholipid. ekuxilongweni

Ngokutsho kweengcali, kophulwe onjalo kurhanelwa kwizigulane ukuya kwiminyaka engama-45 ukuba babe istrowuku okanye iposi engabalulekanga sele unesifo. Kulo mzekelo, oogqirha Siyaleza ngamandla uviwo olupheleleyo ukuqinisekisa okanye, icala, ukukhanyela ingxaki ezifana antiphospholipid syndrome. Cazulula kule meko badlale indima ebalulekileyo. Ngenxa yoko, laboratory ubungqina izifo phambi antibodies iintlobo ezahlukeneyo phospholipids ngokusebenzisa kokubizwa-ezinxulumene enzyme-kulingwa immunosorbent.

Yintoni ekufuneka ziphathwe?

Into ephambili lokuqala kufuneka ibe ukufumanisa isifo, nto leyo eyakhokelela ngqo kuphuhliso antiphospholipid syndrome. Ukusebenza kwalo unyango kukuba ukunciphisa isixa antibodies phospholipids. Ukongeza, imithi banoxanduva ukuhla coagulation umthamo wegazi (umz, iiarhente antiplatelet), kwakunye namachiza antihistaminic (ukunciphisa isimo uyalisa). Ukuba yafunyanwa anda umxholo in vitro negazi omzimba, ngenxa yoko, kuvela ingozi thrombosis ahlekise. Xa olu hlobo meko ngokufuthi abayabelwe plasmapheresis. Abafazi zikarhulumente unesifo onjalo kufuna sifo ekhawulezileyo kunye nolawulo ngokupheleleyo phezu ukukhulelwa. Ukuthintela uphuhliso iingxaki kwezinye iimeko isetyenziswa iziyobisi.

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