ZempiloDiseases and nemibandela

Le anomaly of Arnold Chiari

Anomaly Arnold Chiari wahamba ekuboneni (ukungathobeli indawo) engenazakhiwo ngomva fossa cranial abenza ngokusebenzisa intamo wamzalela enkulu ngaphandle ukakayi kungena lomsele spinal. A shift tonsils cerebellar okanye inxalenye ukhangele nakumphezulu lomsele vertebral.

Kukho iindidi ezine kwesi sifo. Anomaly Arnold Chiari Type 1 iyaboniswa lisisiqalo tonsils cerebellar, ezingahambi luphuhliso mgaqweni kwengqondo olongezelelweyo. Olu hlobo kubonakala kubantu emva kweminyaka engamashumi amathathu. Uhlobo lwesibini waphula iindawo zezakhiwo kwi fossa ngomva kunye tonsils cerebellar. Amaninzi olu hlobo banesifo ebantwaneni. Uhlobo lwesithathu iindawo anomaly of zibandakanya Kukwaphula phantse zonke ezintweni fossa zadnecherepnoy. Okubonakalisa olu hlobo ayi hambelani ebomini. Uhlobo lwesine anomaly inikeze kugqalwa ukutshintshwa ngokukhethekileyo umba wokungaphuhliswa kwiCerebellum. neurosurgery Modern anganibalisela Dandy-Walker syndrome.

Xa isibotho kwiCerebellum kwinxalenye eliphezulu lomsele spinal kukho ukuphazamiseka utywala ephumayo eqhelekileyo ekhusela ingqondo kunye umnqonqo. Ukungaqheleki xa CSF kwegazi kunokubangela ukuvaleka ukuva lobuchopho amalungu okanye ukuqokelelana ulwelo fluid. Uxinzelelo ukuba kwiCerebellum okukuchaphazela umnqonqo kungabangela syringomyelia.

Ngokutsho iingcali ezininzi, Arnold Chiari anomaly uthathwa ukuba isifo njengelifa. Nakuba kunjalo, kufanele kuqatshelwe ukuba izifundo ezijolise uphando le into, ngaba kwi isanda.

Izigulane ezininzi nokubandezeleka kulo disorder, oko kwenza imiqondiso okanye zimpawu waphawula. izigulane asifumanayo akukho unyango. Efumanise sifo lwenzeka kuphela lokufunyaniswa nezinye izifo.

Uphuhliso sifo kwiimeko ezininzi kunye intloko ebuhlungu, nomsindo ukukhohlela, uthimla okanye overexertion ngokwasemzimbeni, imilenze ukuntlontlozela ezandleni, besaphula lobushushu-onovakalelo kwaye ngenxa yoko, ukutsha rhoqo. Ngaphezu koko, ngokuba sisifo esibonakala intlungu wesibeleko kummandla okanye wesibeleko, ukuba izidanga, ngamathuba athile emagxeni. Kukho ubunzima ekulondolozeni imali eseleyo (iqinelwa engalinganiyo) kunye buthathaka uququzelelo ngesandla.

Ngokuba ngenxa yakhe abaninzi iimpawu zesi sifo unxulunyaniswa nezinye izigulo, kuyimfuneko ukuba afunyaniswe isifo epheleleyo.

amanyathelo zokuChonga kuqale uviwo yaye interview nomonde. Ukuba isigulane ikhalazela iintlungu entloko, kodwa isizathu sokuba kwazo Akucaci ke ukuba umntu abanezakhono, iya yabelwe MRI. Uxilongo ivumela ngokwaneleyo ukuchonga ngokuchanekileyo phambi sifo.

Kwezinye iimeko, Arnold Chiari anomaly uba isifo esiqhubeka ekhokelela iingxaki ezinkulu kakhulu. Ezi ziquka hydrocephalus (fluid kwemfuneko ubuchopho). Ngoko ke kukho imfuneko yokuba ityhubhu obunokuguquka zokumpompa ulwelo lwe-cerebrospinal kwenye indawo emzimbeni. Iingxaki esi sifo nazo zibandakanya ukukhubazeka. Yenzeka ngenxa ucinezelo spinal. Syringomyelia sinxulumene naye kubunzima kunokwenzeka. Oko kukhatshwa ukuyilwa cysts emqolo okanye umngxuma, nto leyo izele cerebrospinal fluid aze anike umsebenzi.

Izigulane kufuneka unyango ukungaqheleki Arnold-Chiari inikwa ngokuhambelana ubungqongqo imeko. Xa ukungabikho kweempawu, ngokuqhelekileyo oqeshwe esweni rhoqo kunye nohlolo. Xa ngokubonakala iimpawu ugqirha ephambili ukubekwa ntlungu. Noko ke, uninzi yonyango sifo lwenziwa intsumpa.

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