ZempiloDiseases and nemibandela

Myelodysplastic syndrome

syndrome Myelodysplastic - iqela lonke kakhulu izifo ezinqabileyo athe anxulunyaniswa wamathambo kakuhle. Lo msebenzi ungundoqo umongo - luphuhliso iiseli zegazi. Esi sifo ezinxulumene kakuhle okanye ukuvelisa elinye okanye ngaphezulu iintlobo zeeseli zegazi - iiseli ezibomvu, iiplatelets okanye leukocytes.

Ngenxa yokusilela kubonakala ngathi loo anaemia, isenza buthathaka kwamajoni omzimba kwaye igazi ekunqandeni, ebangela ukopha omkhulu. Myelodysplastic syndrome kunokuba zamabanga kukhula ngokuzenzekelayo, ngaphandle kwesizathu. Ngoxilongo kunye ezinkulu - secondary, leyo zibangelwa zokukhanya, esebenzisa arhente iikhemikhali ndlongo, njl Kufuneka kuqatshelwe ukuba ngokufuthi kakhulu myelodysplastic syndrome zibe wegazi.

Isifo ixhaphakileyo axilonge engama-60, ubuncinane phakathi kweendidi labemi - kubantu abatsha, kwaye kuphela kwiimeko ezinqabileyo kakhulu ebantwaneni.

syndrome Myelodysplastic: iimpawu. Loo sifo kwiimeko ezininzi ithatha indawo efihlakeleyo yaye yafunyanwa ngengozi ngethuba loviwo okanye unyango nezinye izifo.

Nakuba kunjalo, iimpawu onaso osisiphumo yokuphazamiseka wamathambo. Ukuba ubungakanani okanye umgangatho iiseli ezibomvu awusafuni ngegazi - kukho anaemia, sikhatshwa ukudinwa, ubuthathaka, ukozela, ukuphelelwa umoya, ukuba nesiyezi. Xa inani elingonelanga leukocytes zimbi kakhulu impendulo omzimba - umzimba abakwazi ukujongana nezona usulelo zilula. Kwimeko zokugxojwa zegazi ukubunjwa ukuba thrombosis okanye rhoqo ukopha, ezo nzima ukuyeka.

Ukongeza, izigulane ezikhala buhlungu, aqaqambayo, ezibukhali ukwehla kobunzima, umkhuhlane rhoqo.

Myelodysplastic syndrome iindlela diagnostic. Ukuze ukubeka uxilongo lokugqibela, ugqirha kufuneka iziphumo zovavanyo kunye nezifundo nomonde. Okokuqala, enze uvavanyo olupheleleyo igazi ukufumanisa sixa-mali kunye nomlinganiselo iiseli zegazi.

Ngoko ke isigulane emiselweyo isifundo ye inwebu ithambo obuchopho. Ukuza kuthi ga ngoku, biopsy, apho ukuprosesa izinto ifunyenwe ukuba isifundo uchonge nokuphazamiseka. Macingo isifo morphological umbandela - it ikuvumela ukuba ukuchaza ukumeka syndrome nebakala yayo yophuhliso.

Kwakhona ezifunekayo kunye nohlalutyo cytogenetic igazi, ngexesha apho uyakwazi ukubona ukuba ingaba utshintsho kwi zofuzo - oku ngundoqo isifo echanekileyo.

syndrome Myelodysplastic: unyango. Ukhetho unyango ixhomekeke imilo kunye kwisigaba sesi sifo, kwaye ubudala yomguli kunye ukubakhona kwezifo ezihamba. Kwiimeko abanomoya esetyenziswa kunye amathamo phantsi kwezakhi kusetyenziswe amachiza. Maxa wambi kuboniswa kokufumana arhente immunomodulatory. Kwimeko zokugxojwa zegazi ukwakheka igazi esetyenziswa njengenyathelo lexeshana.

Kwezinye iimeko, iyeza kunokwenzeka kuphela - a ithambo ngumongo esinye okanye stem cell intshayelelo. Oku ifana kuphela unyango ukuba ukuphumeza ukuphucuka ixesha elide emzimbeni. Ngelishwa, imisebenzi enjalo kuphela kwizigulane abangaphantsi kweminyaka engama-60 ubudala, yaye, njengoko sele kuchaziwe, malunga neminyaka ezi zifo abafunyenwe kakhulu qho.

syndrome Myelodysplastic: sase-. Umba ezinxulumene kwaba nzima ukunika impendulo ecacileyo, ekubeni kubalulekile ukuqwalasela kwimeko nganye ngokwahlukeneyo sifo. Impumelelo unyango ixhomekeke yobudala yesigulane, uhlobo kwesifo kunye namanye bokuqonda ezininzi.

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