Zempilo, Diseases and nemibandela
Rossolimo-Melkersson-Rosenthal syndrome: Iimpawu, Treatment
Melkersson-Rosenthal syndrome Oku kubizwa isifo esinganyangekiyo, kunye oneziqu iimpawu ezingundoqo. Le ngezifo kwegama kukho amagama amabini oogqirha. Melkersson wachaza iimpawu ezimbini, nesahlulo sesithathu ephawulwe Rosenthal. Ngenxa yoko, esi sifo kuthiwa emva kokuba oogqirha ezimbini.
Kwi Melkersson-Rosenthal syndrome
syndrome polyetiological. Kubaluleke kakhulu kuphuhliso waso eziliqela:
- komzimba esosulelayo;
- iingxaki vasomotor kanye nezici ilifa kubo;
- ngezifo yenkqubo emithanjeni kwindawo yentloko nentamo;
- nakujoliso olutsha ezingapheliyo zosulelo odontogenic;
- sinusitis.
Phambi Melkersson-Rosenthal syndrome yi neuro-sisiba mandundu kunokwenzeka genesis yayo. Ukwenzeka sifo ngamaxesha athile onyaka. Ikakhulu isuka Melkersson-Rosenthal syndrome kuchaphazela abantu abaphakathi 25 nama-35 eminyaka ubudala. Kungabangela i emzimbeni izifo kakubi kotywala, kwakunye nenani iziyobisi. ukubandakanyeka mazwe eqhelekileyo - 75% yazo zonke iimeko. kunqabile kakhulu - lubangelwe.
Iimpawu Melkersson-Rosenthal syndrome
Syndrome wabonakalisa ekweneni imilebe nezidlele. Koko isiya iphela imisipha yobuso. Umntu uba nzima ukuvala amehlo, thetha, iimbombo emlonyeni wathulula ulwelo. Ngowe-30 ekhulwini izigulane ukuphuhlisa amehlo ezomileyo okanye anzongonzongo. Malunga ne-20% - eyomeleziweyo abayibona ngayo izandi kangangokuba kuba krakra. Yintoni enye ubeluphawu iimpawu syndrome Melkersson-Rosenthal? Phantse 80% ezigulane ukongeza ekweneni imilebe babone kwaqapheleka wabo womelele, ukunyuka ulwimi, umphezulu waso uba obungalinganiyo, benqumla. Isiqingatha izigulane abanengxaki yintloko ebuhlungu, ahlaselwe rolls.
Yintoni enye lubonakala ngokuba zokugula?
Ziintoni iimpawu Palsy syndrome ebonakala Rossolimo-Melkersson-Rosenthal? Ekuqaleni, kubalulekile ukukhankanya ukuba Rossolimo - ligama ugqirha wesithathu, owathi ngo-1901 wachaza makroheylit (disease umlomo, ukwandisa ubungakanani) zidityaniswe yobuso nemithambo paresis. Kamva wenza Melkersson. Kodwa ke, ekubeni izifo inkcazelo Rossolimo igama lakhe ngamanye amaxesha asetyenziswe ngezifo yesihloko.
syndrome Cerebral etyhilwe iimviwo njongo. It ungaboniswa ngolu hlobo:
- ebuhlungu (migraine);
- asymmetry yobuso ;
- ekukhubazekeni zobuso imisipha yobuso ;
- uphawu lagophthalmos Bell;
- xerophthalmia;
- hyperacusis;
- dysarthria;
- nokudumba angioneurotic bobuso (idla ngokuba imilebe);
- ulwimi ambe kunye macroglossia;
- dizgevzii kunye ageusia;
- cheilitis granulomatous.
Njengoko waveza syndrome?
Melkersson-Rosenthal syndrome, nto leyo eye iifoto kweli nqaku kumiselwa uxilongo. Kulo mzekelo, ebanjwe:
- kuvavanyo lenzululwazi yegazi;
- X-reyi, ukuba kukho urhano lokuba esi sifo iye yakhula ngenxa kwezifo ezosulelayo (HIV, negcushuwa, isifo Lyme, sarcoidosis);
- electromyography;
- Magnetic intlokoma umfanekiso yobuchopho;
- loviwo zomzimba.
course
Njani na isifo Melkersson-Rosenthal? Syndrome luqala ekweneni ulusu. Ngoko ke Ukhuthaza ukuba isifo ngomlomo. Yandisa ngobukhulu iindevu: top - ngaphezulu asezantsi - ngaphantsi. Mhlawumbi iintlungu le luvo yobuso, yaye kamva ukuphuhlisa ukukhubazeka.
Isifo luphawulwa ukuqala oyingozi. Ukudumba iphuhlisa iiyure eziliqela. Ngokuqhelekileyo olunzulu kunye ngokupheleleyo ithumba imilebe, ezo zipeyintwe obomvu eqaqambileyo, ithinti maxa wambi esiluhlaza ibonakala. Ehlabathini emlonyeni zibe neentanda. intetho aphazamiseka, ubunzima ngokudla.
Njani sisifo esingapheliyo ze Melkersson-Rosenthal? Le syndrome kwakhona iqala ukudumba. Kodwa ke rhoqo, kwandisa kuphela okanye kuyancipha ngamaxesha. Nokudumba egcinwe bonke ubuso kunye kwisisu ngomlomo.
It is a uhlobo engaqhelekanga Melkersson-Rosenthal syndrome, xa izidlele idumbile kuphela. Ngokwesiqhelo, le nje ngomnye wabo. On nemihlathi ngaphakathi sihleli ngokucacileyo amazinyo. Le meko ekuthethwa ngalo elithi "isibini granulomatous." Akukho zimpawu komtshiso oko.
unyango
Njani Melkersson-Rosenthal syndrome? Oogqirha basebenzisa iindlela utyando okanye endilisekileyo. Ekuqaleni, isigulane ndimncinile ukubhaqa ezimbi ukuba kunokubangela izifo. unyango Surgical akuthinteli ukwenzeka, kwaye zisetyenziswa ngakumbi iinjongo izithambiso, xa inyama leyo excised imilebe.
Xa emasikweni unyango iziphumo ezingcono aokusetyenziswa kunye indibaniselwano corticosteroids, elwa namachiza seengcongconi. "Prednisolone" unikwe kunye ne "Oxytetracycline". Faka pyrogenic kunye arhente desensitizing. unyango NJALO virus. Ukuba isigulana uvakalelo staphylococcus, ngoko isebenza "toxoid".
Nomonde ukuba Melkersson-Rosenthal syndrome, iimalthivithamini olugunyazisiweyo ebekiweyo, calcium pantothenate, nicotinic acid, vitamin A, abizwa ngokuthi "komplamin" Kuba ekuphuculeni igazi emzimbeni ezithambileyo. ukusetyenziswa kwekhosi - iintsuku ezili-10. A "Cavintonum", "Tanakan" elimisiweyo kakuhle yaye "stugeron" athathwe ukusuka kwiinyanga 1 ukuya 2. Izigulane alahlwa njenge "Nerobolum". Eli lichiza ethintela ukwaluphala. Amiselweyo okudambisa kunye nadlamkisayo.
Treatment ekula
Ziziphi ezinye iindlela ezinokusetyenziswa ukoyisa syndrome Melkersson-Rosenthal? Unyango kungaba mlonyeni. Ngelo xesha wenza isicelo ze lweeHedfowuni, linamafutha aqholiweyo. Xa zizonke kunye Dimexidum, eshiya kangangemizuzu engama-20. Le nkqubo yenziwa amaxesha 3 ukuya 4 yonke imihla. Ikhosi - iiveki 3-4.
Kuba imilebe esezantsi kusetyenziswa lweeHedfowuni elektrofarez. Lenquba yenzelwa yonke imihla. Xa kusetyenziswa imisinga fizlechenii UBernard, a laser helium-ze neon ultrasound.
Ukusetyenziswa corticosteroid kunye methyluracyl namafutha asetyenziswa kwinkqubo arhabaxa. ubuso imaski isicelo sesibonelelo imizuzu engama-20, amaxesha-2 ukuya kwemi-3 imihla. Ukongeza, izicelo zenziwa mali keratoplasty.
Faka ukuvimba (3-4 ml),-amabini ekhulwini efudumeleyo lidocaine, novocaine kunye trimecaine. Iinaliti zenziwa imihla okanye zonke iintsuku ezimbini.
Iziphumo Melkersson-Rosenthal syndrome
Syndrome ngokukhawuleza uba ezingapheliyo. Oku kubonakala kakhulu xa imbonakalo yomntu, nto leyo egqwethekileyo futhi ekhubazekile ukudumba. Phantsi kwale mvelaphi basoloko ingaba unokudakumba nokuphazamiseka engqondweni. Ngenxa yokwanda nokungakwazi komlomo kunye indoda nzima ihlafuna kunye igwinya, ubugqwetha intetho uyabonakala. Ayangena ukuba kuvela xa ukudumba kwaye kwenzeka iintsholongwane eziyingozi ezibangela izifo ezosulelayo. Oku kukwasebenza ulwimi. Maxa wambi igutyungelwe ukuqhekeka. Ukongeza, le ngozi ukunyuka ngenxa yokulimala amazinyo isifo edematous, umzekelo, xa ihlafuna ukutya.
Abantu abanengxaki kwesi sifo, kucetyiswa ukuba badle ukudla okuqinileyo ngakumbi: Kuza qhutywa iikhosi kuqala, kukho iindidi okuziinkozo kunye neemveliso zobisi. Oku kulula ukuhlafuna ukutya yaye kunciphisa amathuba yokwenzakala ukuya isifo ngomlomo. Iziqhamo nemifuno nazo luncedo, kodwa kufuneka lisikwe kwi izilayi ezincinane kwaye ufake salads. izigaqa amakhulu nawuphi na ukutya kubhetele ukucola ngokusetyenziswa ukutya zokutya.
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