Ukubunjwa, Isayensi
Yintoni neuron motor?
Motor neuron iseli, mvisiswano leyo, kwelinye icala, unoxanduva umsebenzi izihlunu. Ngenxa kokutshatyalaliswa iiseli abanjalo buthathaka, ukuchitha kwezihlunu. Yobuchopho Disease - unesifo esinganyangekiyo ekugqibeleni kukhokelela ukufa isigulane.
iimpawu
Izigulane neuron kabani ziimoto kwi nisaqala parameter nganye, swi nga va iimpawu okucacileyo. Nangona kunjalo, kukho ezinye iimpawu zokuqala ingenzeka kwesi sifo: isigulana kukho ubuthathaka zezihlunu, kuba nzima ukuwusa kwaye ugcine imali eseleyo. Kudla kukho ingxaki yokuginya. Nzima ukugcina nayiphi na into, nokuba akuyi kuba nzima kunene. Ekuhambeni kwexesha, iimpawu zibe ucaca ngakumbi. Kwezinye iimeko, le neuron motor nokuba wambetha ngesandla mnye, kodwa kamva ngezifo kudlulela zombini imilenze. Kwezinye izigulane esi sifo iphuhlisa ukuxhuzula. Le uphawu kubonisa ukuba yonakele imoto neuron asezantsi. Inani elikhulu lezigulane nale ukudinwa Uxilongo kunye buthathaka kwezihlunu kwenzeka kuphela iingalo kunye nemilenze, kodwa practice kukho iimeko ukudinwa yobuso nasemqaleni kwizihlunu, nto leyo ekhokelela nobunzima ligwinya. Uninzi izigulane, nkqu zigaba kade sifo ukugcina ikhono ukucinga kakuhle. Esi sifo ayikho esosulelayo okanye wentsholongwane egazini, ukuba Awunokosulelwa ngabanye, kodwa usesichengeni isifo motor neuron amadoda abaneminyaka eyi-40 ukuya kuma-70. Iminyaka yokuphila yabantu nale unesifo ngokusoloko ungqamane ixesha lokuphila komntu esempilweni. Izazinzulu wayeqhuba isifundo kwaye wafumanisa ukuba 100 amawaka abantu 6 kuphela ukubandezeleka apho kwesi sifo.
Ezibangela isifo
Izizathu ukutyhileka esi sifo kusekho impikiswano phakathi iingcali zonyango sele kuqhutywa. Ngenxa yoko, akukho impendulo ecacileyo lo mbuzo, kwaye kungacaci, nto leyo esisizathu sokuba kukho esi sifo. Ngomhla ezibangela esi sifo abeke phambili iingcebiso ezimbalwa. Omnye wabo - impembelelo iintsholongwane, ubuthi izinto ezinobungozi kokusingqongileyo. Okwesibini, oonobangela kuthelekelelwa - yemfuza, ezizezi ubukho mutating isakhi kwiintsapho.
Motor isifo neuron kungenziwa ngeendlela ezahlukeneyo ukuzibonakalisa ngeendlela ezahlukeneyo. ukusoloko Single kwimbali esi sifo kukuba zonke iintlobo kunye neentlobo ugudle ezivakaliswe ukonakala kwazo luvo lwemoto le nomqolo nobuchopho. Ezi zifo ephambili neuron ezi lateral sclerosis, sclerosis ephambili sclerosis, yoma oluqhubekayo eqatha, pseudobulbar ofe umzimba, kunye yoma spinal dystrophy. Enye yezona zinto zibangela le sifo abantwana babe nesifo wentsholongwane egazini - yipoliyo okanye ukushwabana bobusana.
lateral sclerosis
Kuyinto oluthile lwesifo motor neuron. Limele ubuthathaka kunye yoma kwezihlunu, sivame ezandleni, kodwa kwakhona ukubonisa ezinyaweni. Iimpawu zokuqala inokuba ezahlukeneyo, kodwa ke abe azilingani. Ngenxa ukuqhubeka kwesifo kuvela iimpawu ezibonakalayo, ezizezi luvo mafutha le umnqonqo zenziwa buthathaka ngaphezu imbangela ukucuthwa izihlunu zomzimba. Ifom okuqhubekayo sifo kuhlala kuphela imisebenzi ethile ingatshintshanga. Le echama ilawulwa, iintshukumo yintliziyo amehlo novakalelo. Amanani abonisa ukuba yi-50% kuphela yabantu abane olu hlobo sifo angaphila kangangeminyaka engama-30, kwisiqingatha eseleyo baxovula kuluhlu ukususela kwiminyaka emi-3 ukuya kwi-10, kuxhomekeke iqondo ukwanda kwesi sifo.
sclerosis Primary sclerosis
Olunye uhlobo lwesifo motor neuron. Olu hlobo esi sifo ihamba ehlafuna kakuhle kunye nokutya yokuginya, kwakunye pronunciation inokutyhefeka. izifo ezinokuba ngengqondo ezifana vukele kunye nokuhleka okungalawulekilyo okanye, kungenjalo, elila. izigulane ezininzi nale fomu yaye musani ubomi iminyaka emithathu.
yoma Progressive spinal
Olu hlobo lwesifo neuron motor kwenzeka kuphela abantu abadala, kunye novakalelo intercalated motor neuron yakhe ayitshintshanga. Olu lolona hlobo anyanisekileyo okuvela sifo. Wafumana kuphela ngabantu abadala ngaphezu kweminyaka engama-25 yaye malunga ne-10% amatyala into njengelifa.
Progressive bulbar palsy
Esi sifo kwenzeka kakhulu alufane kunezo zangaphambili. Oko kukhatshwa ngokoyiswa kuphela phezulu zemithambo-luvo. Isifo kubonakala ngcembe kwaye iqala nobuthathaka kwezihlunu kunye aqaqambayo. Esi sifo kwenzeka iminyaka emininzi, ngokuthe ngcembe leyo isigulane yokukhubazeka ngokupheleleyo.
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