ZempiloDiseases and nemibandela

Ventriculomegaly umbungu - ntoni na?

Ventriculomegaly umbungu - yinto leengxaki okwenzeka kwinkqubo ventricular, ngaloo ndlela kusandiswa ubungakanani lateral ventricles lobuchopho, kodwa ingqondo ayinyuki. Kulo sifo ubungakanani le ventricles osecaleni, kunokuba ububanzi yabo ibe ukuya kwi-15 mm.

Ventriculomegaly umbungu ifana siphene ekwanti ngokupheleleyo, kwaye zidityaniswe nezinye okungahambi aziwayo. Kwakhona kuba licandelwana le-mgceni chromosomal kunye malformations ezininzi.

Ngethuba lokwenza uphando kwafunyaniswa ukuba kukho ventriculomegaly ekwanti ndingekazalwa, ngoko amathuba mgaqweni chromosomal usezantsi kakhulu kunokuba ukuba kwenzeka kubanjiswene namanye utshintsho. Kwakhona, njalo isiboniso chromosomal engeyoyesiqhelo ixhomekeke Ububanzi ventricles osecaleni, kunye ukuncitshiswa wabo amathuba ubhaqo iba ngaphezulu.

Ekwenzeni izifundo zesayensi ziye zasekwa ukuba isehlo esi sifo malunga ne-0.6%. Ventriculomegaly umbungu banesifo ngokuqhelekileyo xa kwiiveki 17-34 zokukhulelwa. Kwakhona, ukuxhomekeka of ezingaqhelekanga chromosomal ngenxa yobudala yomguli, okhulelwe oselula, adibana izihlandlo ezithathu ngaphantsi okuba kwezo iminyaka engaphezu kwama-35 ubudala.

Ngenxa yoko, ngoku wafumanisa ukuba zokufumanis ventriculomegaly kwimveku alisilingene kuphela ultrasound, kukho imfuneko karyotyping olungekazalwa.

Kwimeko yokuba uvavanyo ultrasonograph ixabiso ventricles zisecaleni ebuchotsheni apho sifo imiselwa, oko kufuneka-10 mm. Kwiimeko ezininzi, ventriculomegaly hayi labonwa nisaqala yokukhulelwa, kwaye isifo yayo kunokwenzeka emhlabeni ekupheleni 2 - ekuqaleni ezintathu 3. Ngokuqhelekileyo, ixesha-avareji ngexesha apho kunokwenzeka ukuxilonga ngokuchanileyo lo anomaly yi kwisithuba seeveki-26 zokukhulelwa.

Ekuqhubeni ngqo ultrasound uphethwe siswini ventriculomegaly imalunga 80%. iziphumo False-HIV malunga ne-9% yazo zonke iisaveyi.

Ngokuqhelekileyo, ugqirha owenza uxilongo siswini, kukho iingxaki yokuqikelela uphuhliso umntwana, owaba imeko antepartum ventriculomegaly ekwanti. Kwiimeko ezinjalo zidluliselwa ukongamela ventriculomegaly ekwanti. Uphuhliso eqhelekileyo kwabantwana kunye nale anomaly yi malunga ne-80%.

Yokufa kwesi sifo yi avareji malunga ne-14%. Malunga ne-80% abantwana babe uphuhliso oluqhelekileyo ngakumbi, 8% lunomahluko aphakathi kwaye malunga ne-10% amatyala ukuphazamiseka ezinzulu-luvo.

Ventriculomegaly e kubelekwa awuvumeli ukuba kanye uqikelelo kakuhle yophuhliso ngakumbi umntwana. sezulu enjalo kufuneka yenziwe ngobuchule nangokugqibelela, kunye nokuqhutywa isifundo kunye nocazululo lweziphumo. usana Ventriculomegaly ikuvumela ukuba ukunika abantu abane-HIV kuphela xa akukho malformations ezidityanisiweyo usana, kukho karyotype eqhelekileyo, kwaye okuhambisa akufuneki waphawula ukwanda ububanzi ventricles osecaleni kunye nobubanzi babo ayidluli 15 mm. Ezinye iingcali zikholelwa ukuba yinkqubo indlela olunye-kunokubangela iingxaki ezininzi kakhulu luvo kuphuhliso yomntwana.

Mhlawumbi unyango ventriculomegaly ihambo siswini inkcubeko yezonyango emzimbeni. Ithwalwa ngokwamabakala ezimbini, kuqala iintsuku 20 wenza umzimba yaye antihypoxants, kwaye ithuba lesibini unyango lwenziwa kuphela bonisa unyango, kujoliswe kwi umthwalo ngentshukumo static kwizihlunu umgangatho zangasese kunye nokubandakanyeka. Phambi ventriculomegaly ezingekazalwa, unyango angaqalisa xa ubungakanani ventricles osecaleni zomyalelo 12 mm.

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